Orotic aciduria
Wraith, J. E. (2001). "Ornithine carbamoyltransferase deficiency". Archives of Disease in Childhood. 84 (1): 84-88. doi:10.1136 ... Elevated urinary orotic acid levels can also arise secondary to blockage of the urea cycle, particularly in ornithine ...
Ornithine transcarbamylase deficiency
"Ornithine carbamoyltransferase deficiency". Archives of Disease in Childhood. 84 (1): 84-88. doi:10.1136/adc.84.1.84. PMC ... Ornithine transcarbamylase deficiency also known as OTC deficiency is the most common urea cycle disorder in humans. Ornithine ... The substrates of the reaction catalyzed by ornithine transcarbamylase are ornithine and carbamyl phosphate, while the product ... Ornithine transcarbamylase deficiency was the final diagnosis of a patient treated in the 15th episode of 1st season of House, ...
Angomonas deanei
"Endosymbiont as supplier of ornithine carbamoyltransferase in a trypanosomatid". Nature. 270 (5632): 52-53. Bibcode:1977Natur. ... and that it helps the host in synthesising the amino acid arginine from ornithine. As more structural and molecular details ... "An endosymbiont positively modulates ornithine decarboxylase in host trypanosomatids". Biochem Biophys Res Commun. 343 (2): 443 ...
Phytotoxin
Phaseolotoxin is a reversible inhibitor of the enzyme ornithine carbamoyltransferase (OCTase; EC 2.1.3.3), which catalyzes the ... Inhibition of ornithine decarboxylase activity by phaseolotoxin: Implications for symptom production in halo blight of French ... Additionally, phaseolotoxin inhibits the enzyme ornithine decarboxylase (EC 4.1.1.17), which is involved in the biosynthesis of ... formation of citrulline from ornithine and carbamoylphosphate in the arginine biosynthetic pathway. Phaseolotoxin is an ...
Limosilactobacillus pontis
Arginine and proline metabolism
Citrulline is made from ornithine and carbamoyl phosphate by ornithine carbamoyltransferase. Arginine is then synthesized from ... or turned into ornithine by ornithine aminotransferase, followed by cyclisation by ornithine cyclodeaminase to form proline. ...
Ornithine transcarbamylase
... (OTC) (also called ornithine carbamoyltransferase) is an enzyme (EC 2.1.3.3) that catalyzes the ... Strautnieks S, Rutland P, Malcolm S (December 1991). "Arginine 109 to glutamine mutation in a girl with ornithine carbamoyl ... "The crystal structures of ornithine carbamoyltransferase from Mycobacterium tuberculosis and its ternary complex with carbamoyl ... "A novel missense mutation in exon 8 of the ornithine transcarbamylase gene in two unrelated male patients with mild ornithine ...
N-acetylornithine carbamoyltransferase
The systematic name of this enzyme class is carbamoyl-phosphate:N2-acetyl-L-ornithine carbamoyltransferase. Other names in ... 2-N-acetyl-L-ornithine carbamoyltransferase. As of late 2007, 4 structures have been solved for this class of enzymes, with PDB ... In enzymology, a N-acetylornithine carbamoyltransferase (EC 2.1.3.9) is an enzyme that catalyzes the chemical reaction ... the two substrates of this enzyme are carbamoyl phosphate and N2-acetyl-L-ornithine, whereas its two products are phosphate and ...
Postpartum psychosis
Cases have been described in carbamoyl phosphate synthetase 1, argino-succinate synthetase and ornithine carbamoyltransferase ...
N-succinylornithine carbamoyltransferase
... (EC 2.1.3.11, succinylornithine transcarbamylase, N-succinyl-L-ornithine ... N2-succinyl-L-ornithine carbamoyltransferase. This enzyme catalyses the following chemical reaction carbamoyl phosphate + N2- ... N-succinylornithine+carbamoyltransferase at the U.S. National Library of Medicine Medical Subject Headings (MeSH) Portal: ... mutation in the active site swaps the substrate specificity of N-acetyl-L-ornithine transcarbamylase and N-succinyl-L-ornithine ...
OTC
... also called OTC gene or ornithine carbamoyltransferase On-tape Catalog, a section of a Microsoft Tape Format file OpenType ... for example in the big bath technique Order to cash process Over-the-counter drug Oxytetracycline Ornithine transcarbamylase, ...
Sex linkage
Ornithine carbamoyltransferase deficiency Wiskott-Aldrich syndrome Various failures in the SRY genes White eyes in Drosophila ...
Congenital disorders of amino acid metabolism
... disease Homocystinuria Tyrosinemia Trimethylaminuria Hartnup disease Biotinidase deficiency Ornithine carbamoyltransferase ...
List of EC numbers (EC 2)
... aspartate carbamoyltransferase EC 2.1.3.3: ornithine carbamoyltransferase EC 2.1.3.4: deleted EC 2.1.3.5: oxamate ... putrescine carbamoyltransferase EC 2.1.3.7: 3-hydroxymethylcephem carbamoyltransferase EC 2.1.3.8: lysine carbamoyltransferase ... ornithine N-benzoyltransferase EC 2.3.1.128: now classified as EC 2.3.1.266 and EC 2.3.1.267 EC 2.3.1.129: acyl-[acyl-carrier- ... N-succinylornithine carbamoyltransferase EC 2.1.3.13: The enzyme has been replaced by EC 6.1.2.2 EC 2.1.3.14: The enzyme has ...
List of MeSH codes (C10)
... ornithine carbamoyltransferase deficiency disease MeSH C10.228.140.163.100.680 - peroxisomal disorders MeSH C10.228.140.163. ...
List of MeSH codes (D08)
... aspartate carbamoyltransferase MeSH D08.811.913.555.275.600 - ornithine carbamoyltransferase MeSH D08.811.913.555.400 - ... ornithine decarboxylase MeSH D08.811.520.224.125.450 - orotidine-5'-phosphate decarboxylase MeSH D08.811.520.224.125.500 - ... ornithine-oxo-acid transaminase MeSH D08.811.913.477.700.800 - succinyldiaminopimelate transaminase MeSH D08.811.913.477. ... aspartate carbamoyltransferase MeSH D08.811.600.130 - aspartokinase homoserine dehydrogenase MeSH D08.811.600.200 - cholesterol ...
List of MeSH codes (C18)
... ornithine carbamoyltransferase deficiency disease MeSH C18.452.100.100.680 - peroxisomal disorders MeSH C18.452.100.100.680.100 ... ornithine carbamoyltransferase deficiency disease MeSH C18.452.648.151.680 - peroxisomal disorders MeSH C18.452.648.151.680.100 ... ornithine carbamoyltransferase deficiency disease MeSH C18.452.648.066.766 - phenylketonurias MeSH C18.452.648.066.766.500 - ...
List of MeSH codes (C16)
... ornithine carbamoyltransferase deficiency disease MeSH C16.320.565.150.680 - peroxisomal disorders MeSH C16.320.565.150.680.100 ... ornithine carbamoyltransferase deficiency disease MeSH C16.320.565.066.766 - phenylketonurias MeSH C16.320.565.066.766.500 - ...
Lysine carbamoyltransferase
Hommes FA, Eller AG, Scott DF, Carter AL (1983). "Separation of ornithine and lysine activities of the ornithine- ... The systematic name of this enzyme class is carbamoyl-phosphate:L-lysine carbamoyltransferase. This enzyme is also called ... In enzymology, a lysine carbamoyltransferase (EC 2.1.3.8) is an enzyme that catalyzes the chemical reaction carbamoyl phosphate ...
Viomycin
Ornithine cyclodeaminase VioQ: Capreomycidine hydroxylase VioE: Permease VioL: Carbamoyltransferase VioR: Transcriptional ... by the carbamoyltransferase homologue VioL. Bycroft BW (1972). "The crystal structure of viomycin, a tuberculostatic antibiotic ...
Biosynthesis
... and this yields ornithine. Then, the enzymes citrulline and argininosuccinate convert ornithine to arginine. There are two ... Aspartate carbamoyltransferase condenses carbamoyl phosphate with aspartate to form uridosuccinate. Dihydroorotase performs ... The acetyl group of acetylornithine is removed by the enzyme acetylornithinase (AO) or ornithine acetyltransferase (OAT), ... and acetylornithine/succinyldiamino pimelate aminotransferase and yield the N-acetyl-L-ornithine. ...