Low-sulfur diet: A low-sulfur diet is a diet with reduced sulfur content. Sulfur containing compounds may also be referred to as thiols or mercaptans.Cystathionine beta synthase: Cystathionine-β-synthase, also known as CBS, is an enzyme () that in humans is encoded by the CBS gene. It catalyzes the first step of the transsulfuration pathway, from homocysteine to cystathionine:Karl Stellwag von Carion: Karl Stellwag von Carion (January 28, 1823 - November 21, 1904) was an Austrian ophthalmologist who was a native of Langendorf, a village in Moravia.-ine: -ine is a suffix used in chemistry to denote two kinds of substance. The first is a chemically basic and alkaloidal substance.Transsulfuration pathway: The transsulfuration pathway is a metabolic pathway involving the interconversion of cysteine and homocysteine, through the intermediate cystathionine.PyridoxineBetaine: A betaine (BEET-ah-een, ) in chemistry is any neutral chemical compound with a positively charged cationic functional group such as a quaternary ammonium or phosphonium cation (generally: onium ions) which bears no hydrogen atom and with a negatively charged functional group such as a carboxylate group which may not be adjacent to the cationic site. A betaine thus may be a specific type of zwitterion.Journal of Inherited Metabolic Disease: The Journal of Inherited Metabolic Disease is a peer-reviewed medical journal covering inherited metabolic disorders. It was established in 1978 and is the official journal of the Society for the Study of Inborn Errors of Metabolism.Lysinuric protein intoleranceSLC19A2: Thiamine transporter 1, also known as thiamine carrier 1 (TC1) or solute carrier family 19 member 2 (SLC19A2) is a protein that in humans is encoded by the SLC19A2 gene. SLC19A2 is a thiamine transporter.Antoine MarfanMethionineNitrile hydratase: In enzymology, nitrile hydratases (NHases; ) are mononuclear iron or non-corrinoid cobalt enzymes that catalyse the hydration of diverse nitriles to their corresponding amidesLivedoLevomefolic acidCobalamin biosynthesis: {{Infobox protein familyMethylmalonic acid