Aminolevulinic acidAminolevulinic acid dehydratase deficiency porphyria: Aminolevulinic acid dehydratase deficiency porphyria (also known as "Doss porphyria," and "Plumboporphyria") is a cutaneous condition, disease can present during early childhood (as well as in adulthood) with acute neurologic symptoms that resemble those encountered in acute intermittent porphyria. The condition is extremely rare, with fewer than 10 cases ever reported.Sideroblastic anemiaGlutamine synthetaseAminoacyl tRNA synthetases, class IIOasl2: 2'-5' oligoadenylate synthetase-like 2 is a protein that in the house mouse is encoded by the Oasl2 gene. The gene is also known as Oasl, M1204 and Mmu-OASL.Stearyl heptanoateBoron trifluorideHemin (given name)Philip Mallory: Philip Rogers Mallory (1885-1975) was an American businessman and the founder of the company that is now known as Duracell International. Rather than making a career in his family's shipping business, he founded his own manufacturing company, the P.Gene transfer agent: A gene transfer agent or "GTA" is a bacteriophage-like element produced by several bacteria that mediates horizontal gene transfer. GTAs package random segments of DNA present in the host bacterium, which can be transduced to a recipient cell.Heme arginateColes PhillipsUroporphyrinogen ICodinaeopsinHydrocarbon keratosis: A hydrocarbon keratosis (also known as "pitch keratosis," "tar keratosis," and "tar wart") is a precancerous keratotic skin lesion that occurs in people who have been occupationally exposed to polycyclic aromatic hydrocarbons.Freedberg, et al.Burst kinetics: Burst kinetics is a form of enzyme kinetics that refers to an initial high velocity of enzymatic turnover when adding enzyme to substrate. This initial period of high velocity product formation is referred to as the "Burst Phase".ACSL6: Acyl-CoA synthetase long-chain family member 6 is an enzyme that in humans is encoded by the ACSL6 gene. Long-chain acyl-CoA synthetases such as ACSL6, catalyze the formation of acyl-CoA from fatty acids, ATP, and CoA.Cys/Met metabolism PLP-dependent enzyme family: In molecular biology, the Cys/Met metabolism PLP-dependent enzyme family is a family of proteins including enzymes involved in cysteine and methionine metabolism which use PLP (pyridoxal-5'-phosphate) as a cofactor.TetraphenylporphyrinSchiff baseSirohaem synthase: In molecular biology, sirohaem synthase (or siroheme synthase) (CysG) is a multi-functional enzyme with S-adenosyl-L-methionine (SAM)-dependent bismethyltransferase, dehydrogenase and ferrochelatase activities. Bacterial sulphur metabolism depends on the iron-containing porphinoid sirohaem.Symmetry element: A symmetry element is a point of reference about which symmetry operations can take place. In particular, symmetry elements can be centers of inversion, axes of rotation and mirror planes.Glutamate-1-semialdehydeProtein primary structure: The primary structure of a peptide or protein is the linear sequence of its amino acid structural units, and partly comprises its overall biomolecular structure. By convention, the primary structure of a protein is reported starting from the amino-terminal (N) end to the carboxyl-terminal (C) end.List of strains of Escherichia coli: Escherichia coli is a well studied bacterium that was first identified by Theodor Escherich, after whom it was later named.ProerythroblastIron-responsive element-binding protein: The iron-responsive element-binding proteins, also known as IRE-BP, IRBP, IRP and IFRPurinosomeMagnesium-protoporphyrin IX monomethyl ester (oxidative) cyclase: Magnesium-protoporphyrin IX monomethyl ester (oxidative) cyclase (, Mg-protoporphyrin IX monomethyl ester (oxidative) cyclase) is an enzyme with system name magnesium-protoporphyrin-IX 13-monomethyl ester,NADPH:oxygen oxidoreductase (hydroxylating) . This enzyme catalyses the following chemical reactionGlycine (plant): Glycine is a genus in the bean family Fabaceae. The best known species is the soybean (Glycine max).Mature messenger RNA: Mature messenger RNA, often abbreviated as mature mRNA is a eukaryotic RNA transcript that has been spliced and processed and is ready for translation in the course of protein synthesis. Unlike the eukaryotic RNA immediately after transcription known as precursor messenger RNA, it consists exclusively of exons, with all introns removed.PyridoxinePhotoimmunotherapy: Photoimmunotherapy (PIT) is a new type of molecular targeted cancer therapy, which allows the selective destruction of cancer cells in mice without any damage to normal tissues. It is a light-based cancer therapy, which was developed by Professor Kobayashi and his colleagues at National Cancer Institute, Bethesda, Maryland.Spectrophotometry: In chemistry, spectrophotometry is the quantitative measurement of the reflection or transmission properties of a material as a function of wavelength.Allen, D.Carbamoyl phosphate synthetaseX-ray magnetic circular dichroismO-phospho-L-seryl-tRNA:Cys-tRNA synthase: O-phospho-L-seryl-tRNA:Cys-tRNA synthase (, SepCysS, Sep-tRNA:Cys-tRNA synthase) is an enzyme with system name O-phospho-L-seryl-tRNACys:hydrogen sulfide 2-aminopropanoate transferase. This enzyme catalyses the following chemical reactionHootenanny Singers: The Hootenanny Singers (for a couple of weeks originally called the Westbay Singers, Westbay English for Västervik) were a popular folk group from Sweden, founded in 1961, and continuing into the 1970s. The group included Björn Ulvaeus, who later was a member of ABBA.Ligation-independent cloning: Ligation-independent cloning (LIC) is a form of molecular cloning that is able to be performed without the use of restriction endonucleases or DNA ligase. This allows genes that have restriction sites to be cloned without worry of chopping up the insert.Ligase: In biochemistry, ligase (from the Latin verb ligāre — "to bind" or "to glue together") is an enzyme that can catalyze the joining of two large molecules by forming a new chemical bond, usually with accompanying hydrolysis of a small pendant chemical group on one of the larger molecules or the enzyme catalyzing the linking together of two compounds, e.g.CO-methylating acetyl-CoA synthase: Acetyl-CoA Synthase (ACS), not to be confused with Acetyl-CoA Synthetase or Acetate-CoA Ligase (ADP forming), is a Nickel containing enzyme involved in the metabolic processes of cells. Together with Carbon monoxide dehydrogenase (CODH), it forms the bifunctional enzyme Acetyl-CoA Synthase/Carbon Monoxide Dehydrogenase (ACS/CODH) found in anaerobic organisms such as archaea and eubacteria.Constitutive enzyme: Constitutive enzymeshttp://goldbook.iupac.
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