*  Nervous System Involvement in Degos Disease | American Journal of Neuroradiology
Degos disease (also known as malignant atrophic papulosis or Kohlmeier-Degos disease) is a rare vasculopathy of unknown origin ... Summary: Degos disease, or malignant atrophic papulosis, is a rare obstructive vasculopathy of unknown origin, characterized by ... CNS involvement in malignant atrophic papulosis (Kohlmeier-Degos disease): vasculopathy and coagulopathy. J Neurol Neurosurg ... Malignant atrophic papulosis (Degos' disease) involving three generations of a family. J Am Acad Dermatol 1997;37:480-484. ...
  http://www.ajnr.org/content/26/3/646.full
*  Degos disease - meddic
Degos disease (also called malignant atrophic papulosis) is a rare vasculopathy that affects the lining of the medium and small ... "Malignant atrophic papulosis (Köhlmeier-Degos disease) - A review" (PDF). Orphanet Journal of Rare Diseases. 8 (1): 10. doi: ... Scheinfeld N (September 2007). "Malignant atrophic papulosis". Clin. Exp. Dermatol. 32 (5): 483-7. PMID 17692056. doi:10.1111/j ... Degos' Disease (Malignant Atrophic Papulosis) as a Fatal Cause of Acute Abdomen : Report of a Case ...
  http://meddic.jp/Degos_disease
*  Research | Degos Disease | Support Network
Lima on Malignant Atrophic Papulosis (MAP) or Degos Disease (DD) 1. This rare disease is an occlusive vasculopathy ... Degos' disease, otherwise known as "malignant atrophic papulosis" is a rare vasculopathy with an unknown etiology characterized ... Definition of the disease: Malignant atrophic papulosis (MAP), described independently by Köhlmeier and Degos et al., is a rare ... malignant atrophic papulosis, livedoid vasculopathy, and immunoglobulin G4-related disease. ...
  https://degosdisease.com/research/
*  Most recent papers with the keyword Laparascopy | Read by QxMD
BACKGROUND: The malignant form of atrophic papulosis (Köhlmeier-Degos disease) is a rare thrombo-occlusive vasculopathy that ... Laparoscopy shows superiority over endoscopy for early detection of malignant atrophic papulosis gastrointestinal complications ... com/read/26527039/laparoscopy-shows-superiority-over-endoscopy-for-early-detection-of-malignant-atrophic-papulosis- ... Eosinophilic ascites is a rare disorder of unknown aethiology and is a part of the syndrome called eosinophilic gastroenteritis ...
  https://www.readbyqxmd.com/keyword/64565
*  Laparoscopy shows superiority over endoscopy for early detection of malignant atrophic papulosis gastrointestinal complications...
The malignant form of atrophic papulosis (Köhlmeier-Degos disease) is a rare thrombo-occlusive vasculopathy that can affect ... MAPMalignantAtrophic papulosisTreprostinilEculizumabLaparoscopy. Background. Atrophic papulosis (Köhlmeier-Degos disease) is a ... The effects of Eculizumab on the pathology of malignant atrophic papulosis. Orphanent Journal of Rare Diseases. 2013;8:185.View ... Degos R. Malignant Atrophic Papulosis. Br J Dermatol. 1979;100(1):21-35.View ArticlePubMedGoogle Scholar. ...
  https://bmcgastroenterol.biomedcentral.com/articles/10.1186/s12876-015-0387-y
*  Degos disease mimicking primary vasculitis of the CNS | Neurology Neuroimmunology & Neuroinflammation
Malignant atrophic papulosis (Kohlmeier-Degos disease): a review. Orphanet J Rare Dis 2013;8:10. ... Neuropathology (brain and spinal cord) revealed extensive CNS vasculopathy, with multiple foci of hemorrhage and infarction ( ... Degos disease (malignant atrophic papulosis) is a rare multiorgan thrombo-obliterative disorder. With systemic disease, median ... The effects of eculizumab on the pathology of malignant atrophic papulosis. Orphanet J Rare Dis 2013;8:185. ...
  http://nn.neurology.org/content/3/2/e206
*  Antiphospholipid antibody syndrome - The Clinical Advisor
APS may also mimic atrophie blanche/livedoid vasculopathy and malignant atrophic papulosis lesions in the occlusion ... Treatment of CAPS is not standardized, due to lack of evidence for treatment of this rare condition. Precipitating factors, ... Current overview of this rare but deadly complication.) Baker, WF, Bick, RL. "The clinical spectrum of antiphospholipid ... Catastrophic APS (CAPS) is a rare (1%) but very serious presentation of APS, which results in multiorgan dysfunction from ...
  http://www.clinicaladvisor.com/dermatology/antiphospholipid-antibody-syndrome/article/593082/
*  For Doctors | Degos Disease | Support Network
Degos disease (malignant atrophic papulosis) is a rare progressive, small and medium size arterial occluding disease, leading ... Broadly speaking, DD is a vasculopathy or an endovasculitis. It is an occlusive arteriopathy involving small-calibre vessels. ... DD, malignant atrophic papulosis, papulosis atrophicans maligna, Kohlmeier-Degos-Delort-Tricot syndrome, Kohlmeier-Degos ... 26 Howsden S.M., S.J. Hodge, J.H. Herndon, R.G. Freeman (1976). Malignant atrophic papulosis of Degos: report of a patient who ...
  http://degosdisease.com/information/for-doctors/
*  An Overview | Information for Doctors | Degos Disease | Support Network
26 Howsden S.M., S.J. Hodge, J.H. Herndon, R.G. Freeman (1976). Malignant atrophic papulosis of Degos: report of a patient who ... The Papulosis atrophicans maligna (Köhlmeier-Degos disease) is a very rare illness. It was described for the first time by ... Neurological complications reported to date are consequences of cerebral vasculopathy (degeneration of the cerebral blood ... 17 Kish L.S., D.P. Bruynzeel (1984). Six cases of malignant atrophic papulosis (Degos disease) occuring in one family. Br J ...
  http://degosdisease.com/information/for-doctors/an-overview/
*  Degos Disease (Kohlmeier Disease, Degos-Kohlmeier Disease, Malignant atrophic papulosis, benign atrophic papulosis, Malignant...
Also, as rare diseases are usually single hits and are easier to define, one might imagine that the cause of DD will be defined ... From a mechanistic standpoint, DD is a disease of blood vessels that is a vasculopathy or an endovasculitis. It is not a frank ... Malignant atrophic papulosis, benign atrophic papulosis, Malignant atrophic papulosis). *By ... Malignant atrophic papulosis, benign atrophic papulosis, Malignant atrophic papulosis) ...
  https://www.psychiatryadvisor.com/dermatology/degos-disease-kohlmeier-disease-degos-kohlmeier-disease-malignant-atrophic-papulosis-benign-atrophic-papulosis-malignantatrophic-papulosis/article/594252/
*  VIRTUAL GRAND ROUNDS IN DERMATOLOGY 2.0: Isotretinoin: Rare Side-Effects
malignant atrophic papulosis (1) * mastocytosis (2) * Melanoma (16) * Melanoma In Situ (1) ... cutaneous collagenous vasculopathy (1) * Cutting (1) * Darier's Disease (2) * Deer Tick (1) ... There are some rare idiosyncratic reactions. We welcome comments here from patients, their families and practitioners.. The ...
  http://vgrd.blogspot.com/2012/02/isotretinoin-rare-side-effects.html
*  VIRTUAL GRAND ROUNDS IN DERMATOLOGY 2.0: June 2012
malignant atrophic papulosis (1) * mastocytosis (2) * Melanoma (16) * Melanoma In Situ (1) ... Discussion: This is a rare lesion. I am not sure if the diagnosis could have been made prior to pathology. Most of these ... cutaneous collagenous vasculopathy (1) * Cutting (1) * Darier's Disease (2) * Deer Tick (1) ...
  http://vgrd.blogspot.com/2012/06/
*  VIRTUAL GRAND ROUNDS IN DERMATOLOGY 2.0: Melanonychia in a Six Year-Old Child
malignant atrophic papulosis (1) * mastocytosis (2) * Melanoma (16) * Melanoma In Situ (1) ... Acrolentiginous melanoma must be very rare in children; but it is relatively easy to rule out. There appears to be some ... cutaneous collagenous vasculopathy (1) * Cutting (1) * Darier's Disease (2) * Deer Tick (1) ...
  http://vgrd.blogspot.com/2005/07/melanonychia-in-six-year-old-child.html
*  VIRTUAL GRAND ROUNDS IN DERMATOLOGY 2.0: May 2012
malignant atrophic papulosis (1) * mastocytosis (2) * Melanoma (16) * Melanoma In Situ (1) ... Case reports such as this may help to define such rare disorders.. Reference:. Interstitial granulomatous dermatitis. Hillary ... cutaneous collagenous vasculopathy (1) * Cutting (1) * Darier's Disease (2) * Deer Tick (1) ... Pathology: There is a superficial and mid-perivascular and interstitial lymphocytic infiltrate with neutrophils and rare ...
  http://vgrd.blogspot.com/2012/05/
*  VIRTUAL GRAND ROUNDS IN DERMATOLOGY 2.0: Herpes Zoster in a 10 year-old
malignant atrophic papulosis (1) * mastocytosis (2) * Melanoma (16) * Melanoma In Situ (1) ... Herpes zoster in children is unusual but not all that rare. There are a few cases of HZ after vaccination for varicella. As he ... cutaneous collagenous vasculopathy (1) * Cutting (1) * Darier's Disease (2) * Deer Tick (1) ...
  http://vgrd.blogspot.com/2017/04/herpes-zoster-in-10-year-old.html
*  VIRTUAL GRAND ROUNDS IN DERMATOLOGY 2.0: Recurrent BCC with Perineural Invasion
malignant atrophic papulosis (1) * mastocytosis (2) * Melanoma (16) * Melanoma In Situ (1) ... is an infrequent but not rare complication of traditionally low-morbidity skin cancers that can lead to catastrophic sequelae; ... cutaneous collagenous vasculopathy (1) * Cutting (1) * Darier's Disease (2) * Deer Tick (1) ...
  http://vgrd.blogspot.com/2012/03/recurrent-bcc-with-perineural-invasion.html
*  VIRTUAL GRAND ROUNDS IN DERMATOLOGY 2.0: Double Helix
malignant atrophic papulosis (1) * mastocytosis (2) * Melanoma (16) * Melanoma In Situ (1) ... I suspect that these lesions are not rare, since I have seen two in a few weeks in a small New England town. Perhaps, these are ... cutaneous collagenous vasculopathy (1) * Cutting (1) * Darier's Disease (2) * Deer Tick (1) ...
  http://vgrd.blogspot.com/2008/03/double-helix.html
*  VIRTUAL GRAND ROUNDS IN DERMATOLOGY 2.0: June 2006
malignant atrophic papulosis (1) * mastocytosis (2) * Melanoma (16) * Melanoma In Situ (1) ... histiocytes and plasma cells with rare eosinophils consistent with arthropod bite reactio n. NOTE : These changes may be seen ... cutaneous collagenous vasculopathy (1) * Cutting (1) * Darier's Disease (2) * Deer Tick (1) ...
  http://vgrd.blogspot.com/2006/06/
*  Livedo reticularis synonyms, livedo reticularis antonyms - FreeThesaurus.com
... malignant atrophic papulosis-like lesions, subungual splinter hemorrhages, and anetoderma (a circumscribed area of loss of ... Livedo reticularis: a rare manifestation of Graves hyperthyroidism associated with anticardiolipin antibodies ...
  https://www.freethesaurus.com/livedo+reticularis
*  Is Your Disease on the RARE List™ - If So, More Bad News! | The Addi and Cassi Fund - Niemann Pick Type C
I wonder if people truly understand what it means if their rare disease or disorder is on the RARE List™? Last week, the Global ... Malignant cylindroma, Malignant eccrine spiradenoma, Malignant fibrous histiocytoma, Malignant germ cell tumor, Malignant ... Bowenoid papulosis, Bowing congenital short bones, Bowing of legs anterior with dwarfism, Bowing of long bones congenital, ... Vasculopathy retinal with cerebral leukodystrophy, Vasquez Hurst Sotos syndrome, Vein of Galen aneurysm, Velocardiofacial ...
  http://addiandcassi.com/disease-rare-list-bad-news/?replytocom=178994
*  Lymphomatoid Granulomatosis
"Lymphomatoid granulomatosis". Rare hematological malignancies. Springer. 2008. pp. 265-72. (This is a concise review of LYG ... Malignant Lymphoproliferative Disorders of the Lung (Low-grade B-cell lymphoma of BALT, diffuse large B-cell lymphoma of the ... Uncommon presentations include white, atrophic plaques or tan nodules. LYG is often distributed diffusely on the extremeties ... Lymphomatoid Papulosis. *Granulomatosis with polyangiitis (Wegener's granulomatosis). *Churg Strauss vasculitis (Churg Strauss ...
  https://www.neurologyadvisor.com/dermatology/lymphomatoid-granulomatosis/article/589271/
*  Emergency & General Dermatopathology Diagnosis Categories and Histology Criteria
Erythema elevatum diutinum (EED): a rare chronic form of fibrosing vasculitis. Erythema elevatum diutinum (EED) is a rare ... lymphocytes & abnormal lymphs plus polys & eos: lymphomatoid papulosis.. *lymphocytes & histiocytes: *lichen nitidus: usually a ... malignant: as a reflection of internal malignancies. *idiopathic erythroderma: elevated serum IgE levels, dermatopathic ... Livido, livedoid, atrophie blanche23: these are physical diagnosis terms with vasculopathy implications *physiologic livido ...
  http://palpath.com/MedicalTestPages/skiner.htm