Abstract 9820: Catheterization Diastolic Pressures Correlate With Diastolic Dyssynchrony in Patients With Single Right...
9 double outlet right ventricles, 4 unbalanced atrioventricular septal defects. Age was 2.8 ± 3.5 years. Catheterization VEDP ... TDI analysis was performed at the level of the atrioventricular valve. Time interval from onset of QRS to peak TDI e' wave of ... No data exist in patients with single right ventricle (sRV) physiology. Goal of this study was to determine if diastolic ... Catheterization Diastolic Pressures Correlate With Diastolic Dyssynchrony in Patients With Single Right Ventricles. Corey ...http://circ.ahajournals.org/content/128/Suppl_22/A9820
NPHP4 Variants Are Associated With Pleiotropic Heart MalformationsNovelty and Significance | Circulation Research
... complete atrioventricular septal defect, double-outlet right ventricle, and abnormal pulmonary venous return were often ... double-outlet right ventricle, atrioventricular septal defects, and caval vein abnormalities. Sequencing of positional ... Some patients with heterotaxy and/or conotruncal defects such as double-outlet right ventricle and TGA, show several mutations ... Patient IV-12 had atrial situs solitus, atrioventricular concordance, and ventriculoarterial discordance namely, double-outlet ...http://circres.ahajournals.org/content/110/12/1564.long
Similar articles for PubMed (Select 24100093) - PubMed - NCBI
... congenitally corrected transposition of the great arteries or double outlet right ventricle with discordant atrioventricular ... The morphologic left ventricle that requires training by means of pulmonary artery banding before the double-switch procedure ... The results of a two-stage double switch operation for congenital corrected transposition of the great arteries with a ... Midterm results after restoration of the morphologically left ventricle to the systemic circulation in patients with ...https://www.ncbi.nlm.nih.gov/pubmed?linkname=pubmed_pubmed&from_uid=24100093
Pedro J. del Nido, MD | Boston Children's Hospital
Analysis of surgical outcome in complex double-outlet right ventricle with heterotaxy syndrome or complete atrioventricular ... Surgical outcome of double-outlet right ventricle with subpulmonary VSD. Ann Thorac Surg. 2001 Jan; 71(1):49-52; discussion 52- ... Surgical management of double-outlet right ventricle with subaortic ventricular septal defect. Semin Thorac Cardiovasc Surg ... Biventricular conversion after single-ventricle palliation in unbalanced atrioventricular canal defects. Ann Thorac Surg. 2013 ...http://www.childrenshospital.org/research/researchers/d/pedro-del-nido
Children | Free Full-Text | Factors Associated with the Need for, and the Impact of, Extracorporeal Membrane Oxygenation in...
... atrioventricular septal defect, transposition, Ebstein anomaly, hypoplastic left heart syndrome, common arterial trunk, ... The following were associated with ECMO: decreased age, heart failure, acute kidney injury, arrhythmia, double outlet right ... double outlet right ventricle, atrioventricular septal defect, transposition, Ebstein anomaly, hypoplastic left heart syndrome ...http://www.mdpi.com/2227-9067/4/11/101
Surgical Approach to Corrected Transposition of the Great Arteries: Background, Relevant Anatomy, Problem
... the left atrium is connected to a right ventricle, from which an aorta arises. Hence, 2 discordant connections occur in ... congenitally corrected transposition of the great arteries or double outlet right ventricle with discordant atrioventricular ... The first L is for an L-looped right ventricle or a right ventricle with a left-hand pattern of internal organization. During ... Therefore, even if a ventricle is present on the left side, it can be identified as a morphologic right ventricle. The right ...https://emedicine.medscape.com/article/904528-overview
Endothelial lineage-mediated loss of the GATA cofactor Friend of GATA 1 impairs cardiac development. - PubMed - NCBI
14.5 with cardiac defects that include double outlet right ventricle and a common atrioventricular valve. Using conditional ... These findings establish a nonredundant requirement for FOG-1 in the outlet tract and atrioventricular valves of the heart that ... that the aorta of the Tie-2-Cre-mediated FOG-1-excised heart arises from the right ventricle. (Original magnification: ×100.) ... hearts at E14.5 show aorta and pulmonary trunk arising from the right ventricle in the mutant. (Original magnification: ×100.) ...https://www.ncbi.nlm.nih.gov/pubmed?term=14614148
Case of the Week - Society for Cardiovascular Magnetic Resonance
Shw was born with Down Syndrome, double outlet right ventricle, complete atrioventricular septal defect and pulmonary stenosis ... with associated double outlet right ventricle (DORV), dextrocardia, subpulmonary stenosis, subpulmonary VSD and PDA. ... Number 14-04: Double chambered right ventricle or apical muscular VSD. History: A 22 year old female was seen for a routine ... A transthoracic echocardiogram depicted a thrombus in the left ventricle.. A CMR exam was then performed to further evaluate ...http://scmr.org/page/caseoftheweekLDGPG
Frontiers | Primary Ciliary Dyskinesia: An Update on Clinical Aspects, Genetics, Diagnosis, and Future Treatment Strategies |...
Patients with heterotaxy may also have complex cardiac defects such as double outlet right ventricle, atrioventricular canal ... Double lung transplantation in situs inversus with Kartagener's syndrome. Paris-Sud University Lung Transplant Group. J Thorac ... Azithromycin for prevention of exacerbations in non-cystic fibrosis bronchiectasis (EMBRACE): a randomised, double-blind, ... double-blind, placebo-controlled studies of non-CF bronchiectasis, also including few cases with PCD demonstrated that ...https://www.frontiersin.org/articles/10.3389/fped.2017.00135/full
Double outlet right ventricle | Springer for Research & Development
Double outlet right ventricle is the 12th most common congenital heart defect (1.5-2.0% of all congenital heart defects). ... Imamura M, Drummond-Webb JJ, Sarris GE, Murphy DJ, Mee RB (1998) Double-outlet right ventricle with complete atrioventricular ... Surgical anatomy of double-outlet right ventricle with situs solitus and atrioventricular concordance. J Thorac Cardiovasc Surg ... Surgical management of double-outlet right ventricle associated with atrioventricular discordance. J Thorac Cardiovasc Surg 76: ...https://rd.springer.com/chapter/10.1007/978-3-7985-1934-3_11
Discordances Between Pre-Natal and Post-Natal Diagnoses of Congenital Heart Diseases and Impact on Care Strategies | JACC:...
2006) Borderline left ventricles in prenatally diagnosed atrioventricular septal defect or double outlet right ventricle: ... repair for borderline left ventricles in pre-natally diagnosed atrioventricular septal defect and double outlet right ventricle ... In a series of double outlet right ventricles, Gedikbasi et al. (29) showed that the type of ventricular septal defect and the ... 2008) Diagnosis and prognosis in double-outlet right ventricle. Am J Perinatol 25:427-434. ...http://www.onlinejacc.org/content/68/9/921
Transcriptional Regulation of Vertebrate Cardiac Morphogenesis | Circulation Research
... with a single atrioventricular valve, VSD, double outlet right ventricle, and a large ASD. Decreased dosage of Pitx2 leads to ... common atrioventricular canal, and double-outlet right ventricle. Genetic analysis of inherited cardiac septation defects has ... resulting in mice with double-outlet right ventricle, a phenotype not observed in FOG-2-deficient mice.86,87,119⇓⇓ This implies ... Nkx2-5/dHand double-null embryos do not form a ventricle, although a small remnant of ventricular tissue can be identified by ...http://circres.ahajournals.org/content/90/5/509
Imad Tabry, MD, FACS | Holy Cross Hospital
The Surgical Management of Double Outlet Right Ventricle Associated with Atrioventricular. Discordance. Presented at the Annual ... Successful Repair of Double-Outlet Right Ventricular, Complete Atrioventricular Canal, and Atrioventricular Discordance ... Danielson, G.K., Tabry, I.F., Fulton, R.E., Hagler, D.J. and Ritter, D.G.: Successful Repair of Straddling Atrioventricular ... The Surgical Management of Straddling Atrioventricular Valve. Read at the Fourth Annual Meeting of the Samson Thoracic Surgical ...https://www.holy-cross.com/imad-tabry-md
Edward Bove, MD | Joe DiMaggio Children's Hospital
"Biventricular Repair for Double Outlet Right Ventricle with Complete Atrioventricular Septal Defect," Controversies in ... "Double Outlet Right Ventricle: Surgical Perspectives," The American Society of Echocardiography Annual Meeting, Washington, DC ... "Current Strategies for Atrioventricular Discordance," UCLA Mattel Children's Hospital, Los Angeles, CA, April 11, 2013. ... "Hypoplastic Left Heart Syndrome: A Benchmark for the Management of the Single Ventricle," Joe DiMaggio Children's Hospital, ...https://www.jdch.com/physicians/b/bove-edward-l
Stephen Sanders | Harvard Catalyst Profiles | Harvard Catalyst
... crisscross atrioventricular relations, double outlet right ventricle and dextrocardia: morphologic, diagnostic and surgical ... Double-inlet single left ventricle: echocardiographic anatomy with emphasis on the morphology of the atrioventricular valves ... Double-outlet right atrium: anatomic and clinical considerations. Ann Thorac Surg. 2007 Feb; 83(2):619-21. PMID: 17257997. ... Bulboventricular foramen size in infants with double-inlet left ventricle or tricuspid atresia with transposed great arteries: ...https://connects.catalyst.harvard.edu/Profiles/display/Person/93699
Frandics Chan | Stanford Medicine Profiles
... the first description of 5th aortic arch in association with atrioventricular septal defect and double outlet right ventricle. ... Excluding ventricles with valvular insufficiency, cardiac outputs derived from outlet valve flow and stroke volumes were more ... We report a double arch vascular ring that is thought to consist of right fourth arch and left fifth arch components, a ... MRI Evaluation of the Right Ventricle in Pediatric Pulmonary Arterial Hypertension 31st Annual Meeting and Scientific Sessions ...https://med.stanford.edu/profiles/frandics-chan
Anatomically corrective repair of complete atrioventricular septal defects and major cardiac anomalies.
... with complex lesions such as double-outlet right ventricle (DORV) or atrial isomerism have been reported in recent years, the ... Although satisfactory results of corrective surgery for atrioventricular septal defects (AVSDs) ... Double Outlet Right Ventricle / mortality, surgery. Endocardial Cushion Defects / mortality, surgery*. Female. Follow-Up ... with complex lesions such as double-outlet right ventricle (DORV) or atrial isomerism have been reported in recent years, the ...http://www.biomedsearch.com/nih/Anatomically-corrective-repair-complete-atrioventricular/11515877.html
Congenital heart disease: current knowledge about causes and inheritance | The Medical Journal of Australia
AV = atrioventricular. AVSD = atrioventricular septal defect. BAV = bicuspid aortic valve. DORV = double outlet right ventricle ... AVSD = atrioventricular septal defect. CoA = coarctation of the aorta. DORV = double outlet right ventricle. IAA = interrupted ... AVSD = atrioventricular septal defect. CoA = coarctation of the aorta. DORV = double outlet right ventricle. HLHS = hypoplastic ... AVSD = atrioventricular septal defect. CoA = coarctation of the aorta. HLHS = hypoplastic left heart syndrome. L-TGA = ...https://www.mja.com.au/journal/2012/197/3/congenital-heart-disease-current-knowledge-about-causes-and-inheritance
Rajesh Punn, M.D. | Stanford Medicine Profiles
The ninth patient had double outlet right ventricle (two ventricles). Timing of surgical intervention was typically predicated ... Eight of the 9 patients had heterotaxy with an unbalanced atrioventricular canal and functional single ventricle. ... The 17 patients with MAPCAs and two ventricles included 5 with CAVC, 4 with corrected transposition, 3 with double outlet right ... The 50 patients with MAPCAs could be divided into two subgroups: (1) single ventricle anatomy (n = 33) and (2) two ventricle ...https://med.stanford.edu/profiles/rajesh-punn
Should we always plan a Fontan completion after a Kawashima procedure?
Underlying anatomy included atrioventricular septal defect , double-outlet right ventricle , pulmonary atresia , ... The two patients who had more than 9 years of follow-up after Kawashima had antegrade flow preserved between the ventricle and ... Two patients died 23 days and 4 years after Kawashima following cardiac reinterventions (one atrioventricular valve replacement ...http://www.biomedsearch.com/nih/Should-we-always-plan-Fontan/21382726.html
Theresa Tacy | Stanford Medicine Profiles
The ninth patient had double outlet right ventricle (two ventricles). Timing of surgical intervention was typically predicated ... Eight of the 9 patients had heterotaxy with an unbalanced atrioventricular canal and functional single ventricle. ... When all four categories were compared (normal left ventricle, normal right ventricle, SV left ventricle, and SV right ... In postnatal life, patients with single ventricle (SV) with morphologic right ventricles have a worse prognosis than those with ...https://med.stanford.edu/profiles/theresa-tacy
Short- and Long-Term Effects of Inhaled Iloprost Therapy in Children With Pulmonary Arterial Hypertension | JACC: Journal of...
... partial atrioventricular canal; and double-outlet right ventricle with patent ductus arteriosus and coarctation of the aorta). ... a double-blind, randomized, placebo-controlled trial. Am J Respir Crit Care Med 165:800-804. ...http://www.onlinejacc.org/content/51/2/161
Congenitally corrected transposition of the great arteries | Radiology Reference Article | Radiopaedia.org
... is a rare cardiovascular anomaly with inversion of the ventricles and great arteries. Epidemiology This anomaly comprises less ... congenitally corrected transposition of the great arteries or double outlet right ventricle with discordant atrioventricular ... atrioventricular abnormality *when associated with a univentricular heart *double inlet right ventricle ... Thus, atrioventricular and ventriculoarterial discordance (double discordance) exists, and although blood flows in the normal ...https://radiopaedia.org/articles/congenitally-corrected-transposition-of-the-great-arteries
The Outcome of Patients With Right Atrial Isomerism is Poor.
Ventriculoarterial discordance or double-outlet ventricle was seen in 56 and 44 % of patients, respectively. Total anomalous ... Cardiac arrhythmias were noted in nine patients (28 %), two of them with atrioventricular block. Cardiovascular surgery was ... Cardiac defects included dextrocardia in 44 % and common atrioventricular valve in 100 % of patients. ...http://www.biomedsearch.com/nih/Outcome-Patients-With-Right-Atrial/22886362.html
2018 ICD-10-CM Diagnosis Code Q20.2: Double outlet left ventricle
Q20.5 Discordant atrioventricular connection Q20.6 Isomerism of atrial appendages Q20.8 Other congenital malformations of ... Double outlet left ventricle. 2016 2017 2018 Billable/Specific Code POA Exempt *Q20.2 is a billable/specific ICD-10-CM code ...http://www.icd10data.com/ICD10CM/Codes/Q00-Q99/Q20-Q28/Q20-/Q20.2