*  Hereditary fructose intolerance - Wikipedia
Hereditary fructose intolerance (HFI) is an inborn error of fructose metabolism caused by a deficiency of the enzyme aldolase B ... This accumulation has downstream effects on gluconeogenesis and regeneration of adenosine triphosphate (ATP). Symptoms of HFI ... "Disorders of Fructose Metabolism". In Saudubray, Jean-Marie; van den Berghe, Georges; Walter, John H. Inborn Metabolic Diseases ... After ingestion, fructose is converted to fructose-1-phosphate in the liver by fructokinase. Deficiencies of fructokinase cause ...
  https://en.wikipedia.org/wiki/Hereditary_fructose_intolerance
*  Essential fructosuria - Wikipedia
The amount of fructose routinely lost in urine is quite small. Other errors in fructose metabolism have greater clinical ... which inhibits the production of glucose and results in diminished regeneration of adenosine triphosphate. Clinically, patients ... "Disorders of Fructose Metabolism". In Saudubray, Jean-Marie; van den Berghe, Georges; Walter, John H. Inborn Metabolic Diseases ... the second enzyme involved in the metabolism of fructose. This enzyme deficiency results in an accumulation of fructose-1- ...
  https://en.wikipedia.org/wiki/Essential_fructosuria
*  PPT - NEONATAL SEIZURES PowerPoint Presentation - ID:595585
Inborn Errors of Metabolism Associated With Neonatal Seizures. Other conditions. *Isovaleric acidemia (sweaty feet, cheesy odor ... adenosine triphosphate and hypoglycemia. Excess of excitatory neurotransmitter. (eg.glutamic acid-excessive excitation) ... Fructose 1,6-diphosphatase deficiency. *Hereditary Fructose intolerance. *Menkes disease (trichopoliodystrophy. *Peroxisomal ... Inborn Errors of Metabolism Associated With Neonatal Seizures. Conditions That Have a Specific Treatment ...
  https://www.slideserve.com/elsa/neonatal-seizures
*  metabolism | Definition, Process, & Biology - The study of metabolic pathways | Britannica.com
... the chief nitrogen-containing end product of protein metabolism in mammals, is formed exclusively in the liver. They cannot ... Metabolism - The study of metabolic pathways: There are two main reasons for studying a metabolic pathway: (1) to describe, in ... The significance of this observation was first realized in the early 20th century when the phrase "inborn errors of metabolism ... Finally, muscles differ in their metabolism. The adenosine triphosphate (ATP) that they use as their immediate energy source ...
  https://www.britannica.com/science/metabolism/The-study-of-metabolic-pathways
*  PPT - Metabolism 10/27/09 PowerPoint Presentation - ID:3351756
Introduction to metabolism. Metabolism is the overall process through which living systems acquire and utilize free energy to ... inborn errors of metabolism. inborn errors of metabolism comprise a large class of genetic diseases involving disorders of ... metabolism of disaccharides sucrose maltose lactose *metabolism of monosaccharides fructose metabolism mannose metabolism ... Adenosine diphosphate, one phosphoester bond and one phosphoanhydride bond. Adenosine monophosphate one phosphoester bond. ...
  https://www.slideserve.com/lahela/metabolism-10-27-09
*  Metabolism - Wikipedia
Anthropogenic metabolism Antimetabolite Basal metabolic rate Calorimetry Isothermal microcalorimetry Inborn error of metabolism ... One central coenzyme is adenosine triphosphate (ATP), the universal energy currency of cells. This nucleotide is used to ... Once inside, the major route of breakdown is glycolysis, where sugars such as glucose and fructose are converted into pyruvate ... Respirometry Stream metabolism Sulfur metabolism Thermic effect of food Urban metabolism Water metabolism Overflow metabolism ...
  https://en.wikipedia.org/wiki/Metabolism
*  Advances in Gas Chromatographic Methods for the Identification of Biomarkers in Cancer
... inborn errors of metabolism). He is currently a postdoctoral fellow at the Department of Molecular Biology, Umea University, ... The ratio of tetramer-to-dimer is maintained by energy production molecules such as adenosine triphosphate (ATP), as well as ... fructose. 0.67. 13. L-valine. 1.52. 14. citric acid. 0.77. 15. ribitol. 0.74. ... This was subsequently applied to the screening of in-born errors of metabolism (IEMs) in infant urine (93). The method ...
  http://www.jcancer.org/v03p0404.htm
*  Glycolysis | Open Access articles | Open Access journals | Conference Proceedings | Editors | Authors | Reviewers | scientific...
Index of inborn errors of metabolism. Description. * Metabolism * Enzymes and pathways: citric acid cycle * enzymes ... The free energy released in this process is used to form the high-energy compounds ATP (adenosine triphosphate) and NADH ( ... β-D-Fructose 1,6-bisphosphate (F1,6BP) File:Beta-D-fructose-6-phosphate wpmp.png File:Beta-D-fructose-1,6-bisphosphate wpmp.png ... Glucose-6-phosphate2− → Fructose-6-phosphate2− 1.67 -2.9 3 Fructose-6-phosphate2− + ATP4− → Fructose-1,6-bisphosphate4− + ADP3− ...
  http://research.omicsgroup.org/index.php/Glycolysis