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*  Hereditary fructose intolerance - Wikipedia
Hereditary fructose intolerance (HFI) is an inborn error of fructose metabolism caused by a deficiency of the enzyme aldolase B ... This accumulation has downstream effects on gluconeogenesis and regeneration of adenosine triphosphate (ATP). Symptoms of HFI ... "Disorders of Fructose Metabolism". In Saudubray, Jean-Marie; van den Berghe, Georges; Walter, John H. Inborn Metabolic Diseases ... After ingestion, fructose is converted to fructose-1-phosphate in the liver by fructokinase. Deficiencies of fructokinase cause ...
  https://en.wikipedia.org/wiki/Hereditary_fructose_intolerance
*  Essential fructosuria - Wikipedia
The amount of fructose routinely lost in urine is quite small. Other errors in fructose metabolism have greater clinical ... which inhibits the production of glucose and results in diminished regeneration of adenosine triphosphate. Clinically, patients ... "Disorders of Fructose Metabolism". In Saudubray, Jean-Marie; van den Berghe, Georges; Walter, John H. Inborn Metabolic Diseases ... the second enzyme involved in the metabolism of fructose. This enzyme deficiency results in an accumulation of fructose-1- ...
  https://en.wikipedia.org/wiki/Essential_fructosuria
*  Neonatal Hypoglycemia - Cancer Therapy Advisor
Defects of Amino Acid Metabolism Inborn errors of metabolism (propionic acidemia, methylmalonic acidemia, glutaric aciduria) ... Because of disruption of the potassium-adenosine triphosphate complex, these infants usually do not respond to diazoxide. ... Fructose 1,6-diphosphatase deficiency Pyruvate carboxylase/phosphoenolpyruvate carboxykinase deficiency Galactose-1-phosphate ... Inborn errors of metabolism. Routine screening and monitoring of blood glucose concentration is not recommended in healthy term ...
  https://www.cancertherapyadvisor.com/pediatrics/neonatal-hypoglycemia/article/620869/
*  PPT - NEONATAL SEIZURES PowerPoint Presentation - ID:595585
Inborn Errors of Metabolism Associated With Neonatal Seizures. Other conditions. *Isovaleric acidemia (sweaty feet, cheesy odor ... adenosine triphosphate and hypoglycemia. Excess of excitatory neurotransmitter. (eg.glutamic acid-excessive excitation) ... Fructose 1,6-diphosphatase deficiency. *Hereditary Fructose intolerance. *Menkes disease (trichopoliodystrophy. *Peroxisomal ... Inborn Errors of Metabolism Associated With Neonatal Seizures. Conditions That Have a Specific Treatment ...
  https://www.slideserve.com/elsa/neonatal-seizures
*  Disorders of Organic Acid Metabolism | SpringerLink
J. B. Sidbury, E. K. Smith, and W. Harlan, An inborn error of short chain fatty acid metabolism, J. Pediatr. 70:8-15 (1967). ... to glutamate coupled with cleavage of adenosine triphosphate to ade-nosine diphosphate, a reaction in the γ-glutamyl cycle, ... W. C. Hülsmann and J. Fernandes, A child with lactacidemia and fructose diphosphatase deficiency in the liver, Pediatr. Res. 5: ... U. G. Oberholzer, B. Levin, E. A. Burgess, and W. F. Young, Methylmalonic aciduria, an inborn error of metabolism leading to ...
  https://link.springer.com/chapter/10.1007/978-1-4684-2673-1_3
*  metabolism | Definition, Process, & Biology - The study of metabolic pathways | Britannica.com
... the chief nitrogen-containing end product of protein metabolism in mammals, is formed exclusively in the liver. They cannot ... Metabolism - The study of metabolic pathways: There are two main reasons for studying a metabolic pathway: (1) to describe, in ... The significance of this observation was first realized in the early 20th century when the phrase "inborn errors of metabolism ... Finally, muscles differ in their metabolism. The adenosine triphosphate (ATP) that they use as their immediate energy source ...
  https://www.britannica.com/science/metabolism/The-study-of-metabolic-pathways
*  PPT - Metabolism 10/27/09 PowerPoint Presentation - ID:3351756
Introduction to metabolism. Metabolism is the overall process through which living systems acquire and utilize free energy to ... inborn errors of metabolism. inborn errors of metabolism comprise a large class of genetic diseases involving disorders of ... metabolism of disaccharides sucrose maltose lactose *metabolism of monosaccharides fructose metabolism mannose metabolism ... Adenosine diphosphate, one phosphoester bond and one phosphoanhydride bond. Adenosine monophosphate one phosphoester bond. ...
  https://www.slideserve.com/lahela/metabolism-10-27-09
*  Metabolism - Wikipedia
Anthropogenic metabolism Antimetabolite Basal metabolic rate Calorimetry Isothermal microcalorimetry Inborn error of metabolism ... One central coenzyme is adenosine triphosphate (ATP), the universal energy currency of cells. This nucleotide is used to ... Once inside, the major route of breakdown is glycolysis, where sugars such as glucose and fructose are converted into pyruvate ... Respirometry Stream metabolism Sulfur metabolism Thermic effect of food Urban metabolism Water metabolism Overflow metabolism ...
  https://en.wikipedia.org/wiki/Metabolism
*  Carbohydrate Metabolism | Article about Carbohydrate Metabolism by The Free Dictionary
Find out information about Carbohydrate Metabolism. Many aspects of biochemistry and physiology have to do with the breakdown ... and synthesis of simple sugars, oligosaccharides, and polysaccharides, and with... Explanation of Carbohydrate Metabolism ... See Adenosine triphosphate (ATP), Carbohydrate, Chitin, Glycogen. Certain carbohydrates cannot be used as nutrients by humans. ... Carbohydrate Metabolism. *Carbohydrate metabolism, inborn errors. *Carbohydrate metabolism, inborn errors. *Carbohydrate ...
  https://encyclopedia2.thefreedictionary.com/Carbohydrate+Metabolism
*  Targeting FBPase is an emerging novel approach for cancer therapy | Cancer Cell International | Full Text
Emery J, Variend S, Howat A, Vawter G. Investigation of inborn errors of metabolism in unexpected infant deaths. Lancet. 1988; ... Allosteric inhibition of rat liver fructose 1,6-diphosphatase by adenosine 5′-monophosphate. J Biol Chem. 1965;240:651-62. ... adenosine triphosphate. BCAAs: branched chain amino acids. BLBC: basal-like breast cancer ... 6BP fructose-1,6-bisphosphate, F2,6BP fructose-2,6-bisphosphate, F6P fructose-6-phosphate, FBPase fructose-1,6-bisphosphatase, ...
  https://cancerci.biomedcentral.com/articles/10.1186/s12935-018-0533-z
*  Advances in Gas Chromatographic Methods for the Identification of Biomarkers in Cancer
... inborn errors of metabolism). He is currently a postdoctoral fellow at the Department of Molecular Biology, Umea University, ... The ratio of tetramer-to-dimer is maintained by energy production molecules such as adenosine triphosphate (ATP), as well as ... fructose. 0.67. 13. L-valine. 1.52. 14. citric acid. 0.77. 15. ribitol. 0.74. ... This was subsequently applied to the screening of in-born errors of metabolism (IEMs) in infant urine (93). The method ...
  http://www.jcancer.org/v03p0404.htm
*  Glycolysis | Open Access articles | Open Access journals | Conference Proceedings | Editors | Authors | Reviewers | scientific...
Index of inborn errors of metabolism. Description. * Metabolism * Enzymes and pathways: citric acid cycle * enzymes ... The free energy released in this process is used to form the high-energy compounds ATP (adenosine triphosphate) and NADH ( ... β-D-Fructose 1,6-bisphosphate (F1,6BP) File:Beta-D-fructose-6-phosphate wpmp.png File:Beta-D-fructose-1,6-bisphosphate wpmp.png ... Glucose-6-phosphate2− → Fructose-6-phosphate2− 1.67 -2.9 3 Fructose-6-phosphate2− + ATP4− → Fructose-1,6-bisphosphate4− + ADP3− ...
  http://research.omicsgroup.org/index.php/Glycolysis
*  Metabolism - wikidoc
Structure of the coenzyme adenosine triphosphate, a central intermediate in energy metabolism. ... Inborn error of metabolism. *Basal metabolic rate. *Thermic effect of food. *Iron-sulfur world theory, a "metabolism first" ... Pilkis S, el-Maghrabi M, Claus T (1990). "Fructose-2,6-bisphosphate in control of hepatic gluconeogenesis. From metabolites to ... The most central coenzyme is adenosine triphosphate (ATP), the universal energy currency of cells. This nucleotide is used to ...
  http://es.wikidoc.org/index.php/Metabolism
*  Mitochondrial Correction: A New Therapeutic Paradigm for Cancer and Degenerative Diseases - isom.ca
J Inborn Errors Metab and Screening, 5.. Eschbach, L.F., Webster, M.J., Boyd, J.C., McArthur, P.D., & Evetovich, T.K. (2000). ... Some important mitochondrial functions are: (a) energy conversion with production of adenosine triphosphate (ATP), (b) ... The transition from glucose metabolism to ketone metabolism is also a powerful anti-inflammatory strategy. The goal of this ... Effects of fructose diphosphate, AMP, ATP and citrate. J Biol Chem, 251(23), 7322-8. ...
  https://www.isom.ca/article/mitochondrial-correction-new-therapeutic-paradigm-cancer-degenerative-diseases/