*  Very long chain acyl-CoA dehydrogenase deficiency
... Common Name(s). Very long chain acyl-CoA dehydrogenase deficiency, VCLAD ... "Very long chain acyl-CoA dehydrogenase deficiency" (open studies are recruiting volunteers) and 9 "Very long chain acyl-CoA ... Very Long-chain Acyl-CoA Dehydrogenase Deficiency; Trifunctional Protein Deficiency; Long-chain 3-hydroxyacyl-CoA Dehydrogenase ... Medium-chain Acyl-CoA Dehydrogenase Deficiency; Multiple Acyl-CoA Dehydrogenase Deficiency; Carnitine Transporter Deficiency; ...
  http://diseaseinfosearch.org/ACADVL/7410
*  Need some antibodies - Immunology - BioForum
... very long-chain acyl-CoA dehydrogenase (VLCAD) short-chain 3-hydroxyacyl-CoA dehydrogenase (SCHAD) medium-chain 3-hydroxyacyl- ... long-chain 3-hydroxyacyl-CoA dehydrogenase (LCHAD) mitochondrial trifunctional protein (MTP/TFP) ... very long-chain acyl-CoA dehydrogenase (VLCAD). short-chain 3-hydroxyacyl-CoA dehydrogenase (SCHAD). medium-chain 3-hydroxyacyl ... long-chain 3-hydroxyacyl-CoA dehydrogenase (LCHAD). mitochondrial trifunctional protein (MTP/TFP) ...
  http://www.protocol-online.org/forums/topic/5772-need-some-antibodies/
*  A severe genotype with favourable outcome in very long chain acyl-CoA dehydrogenase deficiency | Archives of Disease in...
... very-long-chain acyl-CoA dehydrogenase deficiency in three patients previously diagnosed with long-chain acyl-CoA dehydrogenase ... 1993) Very-long-chain acyl-CoA dehydrogenase deficiency: identification of a new inborn error of mitochondrial fatty acid ... Very long chain acyl-CoA dehydrogenase (VLCAD) deficiency is a recently identified inborn error of a membrane bound ... 1993) A novel disease with deficiency of mitochondrial very-long-chain acyl-CoA dehydrogenase. Biochem Biophys Res Commun 191: ...
  http://adc.bmj.com/content/84/1/58
*  PatientsLikeMe | Very long chain Acyl-CoA dehydrogenase deficiency symptoms, treatments & patient forums | PatientsLikeMe
2 patients with very long chain Acyl-CoA dehydrogenase deficiency experience fatigue, insomnia, depressed mood, pain, and ... Find the most comprehensive real-world symptom and treatment data on very long chain Acyl-CoA dehydrogenase deficiency at ... What is very long chain Acyl-CoA dehydrogenase deficiency?. Very long chain acyl-coenzyme A dehydrogenase deficiency is a ... Who has very long chain Acyl-CoA dehydrogenase deficiency on PatientsLikeMe?. * 2 patients have this condition ...
  https://www.patientslikeme.com/conditions/2525-very-long-chain-acyl-coa-dehydrogenase-deficiency
*  Acadvl - Very long-chain-specific acyl-CoA dehydrogenase, mitochondrial - Mus musculus (Mouse) - Acadvl gene & protein
PF00441. Acyl-CoA_dh_1. 1 hit. PF02770. Acyl-CoA_dh_M. 1 hit. PF02771. Acyl-CoA_dh_N. 1 hit. ... PF00441. Acyl-CoA_dh_1. 1 hit. PF02770. Acyl-CoA_dh_M. 1 hit. PF02771. Acyl-CoA_dh_N. 1 hit. ... Very long-chain-specific acyl-CoA dehydrogenase, mitochondrialImported. ,p>Information which has been imported from another ... tr,B1AR28,B1AR28_MOUSE Very long-chain-specific acyl-CoA dehydrogenase, mitochondrial OS=Mus musculus GN=Acadvl PE=1 SV=1 ...
  http://www.uniprot.org/uniprot/B1AR28
*  Long-chain acyl-CoA dehydrogenase - Wikipedia
Long-chain acyl-CoA dehydrogenase (EC 1.3.8.8, palmitoyl-CoA dehydrogenase, palmitoyl-coenzyme A dehydrogenase, long-chain acyl ... long-chain-acyl-CoA:(acceptor) 2,3-oxidoreductase, ACADL (gene).) is an enzyme with systematic name long-chain acyl-CoA: ... medium-chain, and long-chain acyl-CoA dehydrogenases from rat liver mitochondria. Isolation of the holo- and apoenzymes and ... Long-chain acyl-CoA dehydrogenase at the US National Library of Medicine Medical Subject Headings (MeSH) Molecular and Cellular ...
  https://en.wikipedia.org/wiki/Long-chain_acyl-CoA_dehydrogenase
*  Very-long-chain acyl-CoA dehydrogenase - Wikipedia
Very-long-chain acyl-CoA dehydrogenase (EC 1.3.8.9, ACADVL (gene).) is an enzyme with systematic name very-long-chain acyl-CoA: ... "Structural basis for substrate fatty acyl chain specificity: crystal structure of human very-long-chain acyl-CoA dehydrogenase ... Very-long-chain acyl-CoA dehydrogenase at the US National Library of Medicine Medical Subject Headings (MeSH) Molecular and ... I. Purification and properties of very-long-chain acyl-coenzyme A dehydrogenase". J. Biol. Chem. 267 (2): 1027-1033. PMID ...
  https://en.wikipedia.org/wiki/Very-long-chain_acyl-CoA_dehydrogenase
*  Very Long Chain Acyl CoA Dehydrogenase Deficiency (VLCAD) | CHEO NSO
Very Long Chain Acyl CoA Dehydrogenase Deficiency (VLCAD)Download version for offline viewing or printing. [480.71kB] ... Very long-chain acyl-CoA dehydrogenase deficiency (VLCAD) is a rare, inherited (genetic) disease. ... Treatment is started as early as possible and is usually life long. Babies with VLCAD have their health and development checked ... Babies with VLCAD cannot make certain fats into energy, especially during long periods without food (fasting). ...
  https://www.newbornscreening.on.ca/en/disease/very-long-chain-acyl-coa-dehydrogenase-deficiency-vlcad
*  Recurrent ACADVL molecular findings in individuals with a positive newborn screen for very long chain acyl-coA dehydrogenase ...
Very long chain acyl-coA dehydrogenase deficiency (VLCADD) is an autosomal recessive inborn error of fatty acid oxidation ... Infants suspected to have very-long chain acyl-CoA dehydrogenase deficiency from newborn screening.. *J Lawrence Merritt, ... Positive newborn screen in a normal infant of a mother with asymptomatic very long-chain Acyl-CoA dehydrogenase deficiency.. * ... Very long chain acyl-coA dehydrogenase deficiency (VLCADD) is an autosomal recessive inborn error of fatty acid oxidation ...
  https://www.semanticscholar.org/paper/Recurrent-ACADVL-molecular-findings-in-individuals-Miller-Burrage/5e68f40d49ef6b427b9f43472ff429a904115cbe
*  Acyl-CoA dehydrogenase, very long chain, deficiency of (Symptoms, signs, causes, treatments & definition) - Medigest
... very long chain, deficiency of? Medigest has all you need to know about Acyl-CoA dehydrogenase, very long chain, deficiency of ... Discuss Acyl-CoA dehydrogenase, very long chain, deficiency of in our forums Discuss Acyl-CoA dehydrogenase, very long chain, ... Acyl-CoA dehydrogenase, very long chain, deficiency of Below you will find more information about Acyl-CoA dehydrogenase, very ... Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCADD) is a rare autosomal recessive condition in which the body fails to ...
  https://www.medigest.uk/diseases/acyl-coa-dehydrogenase-very-long-chain-deficiency-of/
*  Characterization of human and pig kidney long-chain-acyl-CoA dehydrogenases and their role in beta-oxidation
Long-chain-acyl-CoA dehydrogenase (LCADH) has been produced by recombinant techniques from the human cDNA and purified after ... Characterization of human and pig kidney long-chain-acyl-CoA dehydrogenases and their role in beta-oxidation. * Home ... Characterization of human and pig kidney long-chain-acyl-CoA dehydrogenases and their role in beta-oxidation. Publikationstyp: ... Characterization_of_human_and_pig_kidney_long_chain_acyl_CoA_dehydrogenases_and_their_role_in_beta_oxidation.pdf. 142. ...
  https://kops.uni-konstanz.de/handle/123456789/7772
*  LCAD (cd01160) | InterPro | EMBL-EBI
Long-chain specific acyl-CoA dehydrogenase (IPR034179) Member database. CDD. CDD is a protein annotation resource that consists ...
  http://www.ebi.ac.uk/interpro/signature/cd01160
*  Search of: 'MERRF Syndrome' OR 'Mitochondrial Myopathies' OR 'myoclonic epilepsy with ragged-red fibers' - List Results -...
High Protein Diet in Patients With Long-chain Fatty Acid Oxidation Disorders. *Very Long-chain Acyl-CoA Dehydrogenase ... Vitamin E Treatment for Long-Chain 3-Hydroxyacyl Coenzyme A (CoA) Dehydrogenase (LCHAD) Associated Neuropathy. *Peripheral ... Very Long-chain Acyl-CoA Dehydrogenase Deficiency. *Trifunctional Protein Deficiency. *Long-chain 3-hydroxyacyl-CoA ... An Outcome of This Study is the Difference in Percent Body Fat (%BF) Between Subjects With a Long-chain Fatty Acid Oxidation ...
  https://clinicaltrials.gov/ct2/results?cond=%22MERRF+Syndrome%22+OR+%22Mitochondrial+Myopathies%22+OR+%22myoclonic+epilepsy+with+ragged-red+fibers%22&show_rss=Y&sel_rss=mod14
*  Search of: Mitochondrial Myopathies - List Results - ClinicalTrials.gov
High Protein Diet in Patients With Long-chain Fatty Acid Oxidation Disorders. *Very Long-chain Acyl-CoA Dehydrogenase ... Vitamin E Treatment for Long-Chain 3-Hydroxyacyl Coenzyme A (CoA) Dehydrogenase (LCHAD) Associated Neuropathy. *Peripheral ... Very Long-chain Acyl-CoA Dehydrogenase Deficiency. *Trifunctional Protein Deficiency. *Long-chain 3-hydroxyacyl-CoA ... An Outcome of This Study is the Difference in Percent Body Fat (%BF) Between Subjects With a Long-chain Fatty Acid Oxidation ...
  https://clinicaltrials.gov/search/term=Mitochondrial%20Myopathies
*  Search of: 'lipid metabolism, inborn errors' OR 'farber lipogranulomatosis' - List Results - ClinicalTrials.gov
High Protein Diet in Patients With Long-chain Fatty Acid Oxidation Disorders. *Very Long-chain Acyl-CoA Dehydrogenase ... Vitamin E Treatment for Long-Chain 3-Hydroxyacyl Coenzyme A (CoA) Dehydrogenase (LCHAD) Associated Neuropathy. *Peripheral ... Very Long-chain Acyl-CoA Dehydrogenase Deficiency. *Trifunctional Protein Deficiency. *Long-chain 3-hydroxyacyl-CoA ... An Outcome of This Study is the Difference in Percent Body Fat (%BF) Between Subjects With a Long-chain Fatty Acid Oxidation ...
  https://clinicaltrials.gov/ct2/results?cond=%22lipid+metabolism%2C+inborn+errors%22+OR+%22farber+lipogranulomatosis%22&show_rss=Y&sel_rss=new14
*  IJMS | Free Full-Text | Comparative Analysis of Mafriwal (Bos taurus × Bos indicus) and Kedah Kelantan (Bos indicus) Sperm...
... glycerol-3-phosphate dehydrogenase and very long-chain specific acyl-CoA dehydrogenase that are related to lipid metabolism ... Very long-chain specific acyl-CoA dehydrogenase, mitochondrial. Bos taurus. 66.1. 6 (4). M specific. -. 551. ... Succinate dehydrogenase flavoprotein subunit (FP) and 60 KDa heat shock protein were found to be M specific. Heat shock ... Glyceraldehyde-3-phosphate dehydrogenase, testis-specific. Bos taurus. 76.8. 14 (5). KK specific isoform. -. 437. ...
  http://www.mdpi.com/1422-0067/14/8/15860/htm
*  Recombinant Human ACADL protein (ab113579) | Abcam
Defects in ACADL are a cause of acyl-CoA dehydrogenase very long-chain deficiency (ACADVLD) [MIM:201475]. An inborn error of ... Long chain acyl CoA dehydrogenase. *Long-chain specific acyl-CoA dehydrogenase, mitochondrial ... mitochondrial fatty acid beta-oxidation which leads to impaired long-chain fatty acid beta-oxidation. It is clinically ... Acyl Coenzyme A dehydrogenase long chain. *Acyl-CoA dehydrogenase long chain. *FLJ94052 ...
  https://www.abcam.com/recombinant-human-acadl-protein-ab113579.html
*  Expression of ACADL in cancer - Summary - The Human Protein Atlas
GO:0003995 [acyl-CoA dehydrogenase activity]. GO:0004466 [long-chain-acyl-CoA dehydrogenase activity]. GO:0005739 [ ... Acyl-CoA dehydrogenase, long chain (HGNC Symbol). Entrez gene summary. The protein encoded by this gene belongs to the acyl-CoA ... Acyl-CoA dehydrogenase, long chain. Protein classi. Protein class the gene product belongs to according to selected gene lists ... Defects in this gene are the cause of long-chain acyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia ...
  http://www.proteinatlas.org/ENSG00000115361-ACADL/pathology
*  Fatty liver and Mucus membrane symptoms - Symptom Checker - check medical symptoms at RightDiagnosis
2. Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency. 3. Woodhouse Sakati syndrome. Show causes with descriptions ». , Start ... 1. 3-alpha-Hydroxyacyl-CoA Dehydrogenase Deficiency. 2. 3-alpha-hydroxyacyl-coenzyme A dehydrogenase deficiency. 3. ACPS III. 4 ...
  https://wrongdiagnosis.com/cosymptoms/fatty-liver/mucus-membrane-symptoms.htm
*  NBS | definition of NBS by Medical dictionary
Very-long-chain acyl-CoA dehydrogenase deficiency. Deficiency of or non-functioning enzyme: very-long-chain acyl-CoA ... Medium-chain acyl-CoA dehydrogenase deficiency. Deficiency of or nonfunctioning enzyme: medium-chain acyl-CoA dehydrogenase. ... Long-chain L-3-hydroxyacyl-CoA dehydrogenase deficiency. Deficiency of or non-functioning enzyme: long-chain L -3-hydroxyacyl- ... Deficiency of or non-functioning enzyme: 3-methylcrotonyl-CoA carboxylase, 2-methylbutyryl-CoA dehydrogenase. 3-hydroxy- ...
  http://medical-dictionary.thefreedictionary.com/NBS
*  In vivo proton T1 relaxation times of mouse myocardial metabolites at 9.4 T. - Semantic Scholar
Carnitine supplementation attenuates myocardial lipid accumulation in long-chain acyl-CoA dehydrogenase knockout mice. * ... Fastinginduced myocardial lipid accumulation in long-chain acyl-CoA dehydrogenase knockout mice is accompanied by impaired left ...
  https://www.semanticscholar.org/paper/In-vivo-proton-T1-relaxation-times-of-mouse-at-9.4-Bakermans-Abdurrachim/b45a6e0a5def719911ba00a1b9c6266b0ce2fa03
*  Muscle aches - RightDiagnosis.com
Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency ... muscle pain*Long-Chain Acyl-CoA Dehydrogenase Deficiency ... ... Lactate dehydrogenase deficiency type A ... muscle cramps*Lambert-Eaton Myasthenic Syndrome ... muscular pain*Lassa fever ... ...
  https://www.rightdiagnosis.com/sym/muscle_aches.htm
*  Human Metabolome Database: Showing metabocard for TG(16:1(9Z)/18:1(9Z)/20:4(5Z,8Z,11Z,14Z)) (HMDB0005441)
Catalyzes the transfer of the acyl group of long-chain fatty acid-CoA conjugates onto carnitine, an essential step for the ... The ER/mitochondria pathway requires the action of glycerol-3-phosphate dehydrogenase to convert DHAP to glycerol-3-phosphate. ... The fatty acids that are incorporated into TAGs are activated to acyl-CoAs through the action of acyl-CoA synthetases. Two ... Functions as the major acyl-CoA retinol acyltransferase (ARAT) in the skin, where it acts to maintain retinoid homeostasis and ...
  http://www.hmdb.ca/metabolites/HMDB05441
*  SOYBEAN VARIETY D2011901 - Patent application
CoA (J. Biol. Chem., 267(9):5931-5936, 1992). Fox et al. describe a gene encoding a stearoyl-acyl carrier protein delta-9 ... A long, curvy sepal covers the keel, and the stigma is on the opposite side of the flower. The calyx is removed by grasping a ... Mannitol-1-phosphate dehydrogenase (mt1D) from E. coli has been used to provide protection against drought and salinity. ... single-chain antibody fragments. Numerous other examples of insect resistance have been described. See, for example, U.S. Pat. ...
  http://www.patentsencyclopedia.com/app/20130042364