FructoseFructokinasesMetabolism, Inborn ErrorsFructose Metabolism, Inborn ErrorsFructosephosphatesFructose-1,6-Diphosphatase DeficiencyAdenosineAdenosine TriphosphateAmino Acid Metabolism, Inborn ErrorsGlucoseReceptor, Adenosine A2AReceptor, Adenosine A1Adenosine DeaminaseReceptor, Adenosine A3Adenosine MonophosphateLipid Metabolism, Inborn ErrorsAdenosine KinaseReceptor, Adenosine A2BFructosediphosphatesAdenine NucleotidesEnergy MetabolismNeonatal ScreeningPurine-Pyrimidine Metabolism, Inborn ErrorsReceptors, Adenosine A2Carbohydrate Metabolism, Inborn ErrorsReceptors, Purinergic P1Steroid Metabolism, Inborn ErrorsAdenosine A2 Receptor AgonistsHexosediphosphatesAdenosine A2 Receptor AntagonistsAdenosine A1 Receptor AntagonistsKineticsGuanosine TriphosphateFructose IntoleranceAdenosine A1 Receptor AgonistsUrea Cycle Disorders, InbornBrain Diseases, Metabolic, InbornLiverPurinergic P1 Receptor AntagonistsReceptors, PurinergicAdenosine TriphosphatasesArgininosuccinic AciduriaPhosphofructokinase-1PhosphatesLipid MetabolismHyperammonemiaGlycolysisAdenosine DiphosphateFructose-BisphosphataseXanthinesTime FactorsMutationMagnesiumPurinergic P1 Receptor AgonistsLactatesTheophyllineApyraseMagnetic Resonance SpectroscopyGlucose Transporter Type 5PhenylketonuriasNucleotidesPhosphocreatineMolecular Sequence DataCalciumSmith-Lemli-Opitz SyndromeHydrogen-Ion ConcentrationUridine TriphosphateMetabolismPhosphorus IsotopesAdenosine-5'-(N-ethylcarboxamide)5'-NucleotidaseInfant, NewbornCyclic AMPPhosphotransferasesCarbon IsotopesReceptors, Purinergic P2Cells, CulturedLactic AcidInosineDose-Response Relationship, DrugPyruvatesRefractive ErrorsOxygen ConsumptionModels, BiologicalHomogentisate 1,2-DioxygenaseRabbitsOxidative PhosphorylationPyruvate KinaseHomocystinuriaCandidiasis, Chronic MucocutaneousBrainAdenosine A3 Receptor AntagonistsPyruvate Metabolism, Inborn ErrorsMyocardiumalpha-GalactosidaseRats, Inbred StrainsRats, Sprague-DawleyCoformycinFabry DiseaseFructose-Bisphosphate Aldolase