snRNP Core ProteinsRibonucleoproteins, Small NuclearMotor NeuronsViral Core ProteinsNeuronsMotor Neuron DiseaseSurvival of Motor Neuron 1 ProteinRibonucleoprotein, U1 Small NuclearNeurons, AfferentCell SurvivalSurvival of Motor Neuron 2 ProteinMotor CortexSurvival RateRibonucleoprotein, U2 Small NuclearEvoked Potentials, MotorMuscular Atrophy, SpinalSMN Complex ProteinsAmyotrophic Lateral SclerosisSpinal CordBiogenesisMolecular Sequence DataSpliceosomesMotor ActivityRNA, Small NuclearMutationAmino Acid SequenceProteoglycansRNA-Binding ProteinsAxonsNerve Tissue ProteinsRNA SplicingRibonucleoprotein, U4-U6 Small NuclearChondroitin Sulfate ProteoglycansCells, CulturedRNA PrecursorsRibonucleoproteinsBase SequenceTime FactorsAction PotentialsDisease-Free SurvivalRibonucleoprotein, U5 Small NuclearHeLa CellsImmunohistochemistrySurvivalMice, TransgenicMolecular Motor ProteinsProtein BindingCell LineRNA, MessengerNerve DegenerationElectric StimulationSynapsesCoiled BodiesNeuromuscular DiseasesGanglia, InvertebrateSurvival AnalysisHepacivirusSignal TransductionElectrophysiologyDisease Models, AnimalMice, Inbred C57BLInterneuronsSynaptic TransmissionMovementSuperoxide DismutaseHepatitis B Core AntigensBrainGraft SurvivalNuclear ProteinsModels, BiologicalCholinergic NeuronsCell NucleusGreen Fluorescent ProteinsAplysiaMitochondrial TurnoverDopaminergic NeuronsAnimals, Genetically ModifiedAnimals, NewbornDecorinMembrane ProteinsMitochondriaTranscription FactorsElectromyographyNeuromuscular JunctionAnterior Horn CellsDendritesBlotting, WesternSensory Receptor CellsProtein Structure, TertiaryGanglia, SpinalMice, KnockoutSequence Homology, Amino AcidPatch-Clamp TechniquesAggrecansBulbar Palsy, ProgressiveProtein TransportNeural InhibitionHeparan Sulfate ProteoglycansGABAergic NeuronsCyclic AMP Response Element-Binding Protein