SMN Complex ProteinsSurvival of Motor Neuron 1 ProteinMuscular Atrophy, SpinalSurvival of Motor Neuron 2 ProteinMotor NeuronsSpinal Muscular Atrophies of ChildhoodCyclic AMP Response Element-Binding ProteinRNA-Binding ProteinsNerve Tissue ProteinsNeuronal Apoptosis-Inhibitory ProteinMotor Neuron DiseaseNeuronsCoiled BodiesRibonucleoproteins, Small NuclearExonsGemini of Coiled BodiesSpinal CordIndoprofenCell SurvivalNeuropil ThreadsDEAD Box Protein 20Neuromuscular Junction DiseasesNeurons, AfferentDisease Models, AnimalMotor CortexAxonsSurvival RateEvoked Potentials, MotorMutationNeuromuscular JunctionMice, TransgenicAmyotrophic Lateral SclerosisRNA SplicingsnRNP Core ProteinsAlternative SplicingMolecular Sequence DataChromosomes, Human, Pair 5Gene DeletionGene DosageCells, CulturedMotor ActivitySpliceosomesFibroblastsHeterozygote DetectionImmunohistochemistryPhenotypeCell LineHomozygoteHeLa CellsBase SequenceProtein-Arginine N-MethyltransferasesCentromereAmino Acid SequencePolymorphism, Single-Stranded ConformationalAction PotentialsMuscle, SkeletalMice, KnockoutRNA, MessengerDisease-Free SurvivalIntronsBlotting, WesternCell NucleusTime FactorsSurvivalProtein BindingMolecular Motor ProteinsNerve DegenerationElectric StimulationPedigreeSynapsesNeuromuscular DiseasesRNAGanglia, InvertebratePolymerase Chain ReactionGene ExpressionReverse Transcriptase Polymerase Chain ReactionSurvival AnalysisElectrophysiologyInterneuronsSynaptic TransmissionGraft SurvivalTranscription, GeneticMovementCholinergic NeuronsSuperoxide DismutaseAplysiaDopaminergic NeuronsElectromyographyAnterior Horn CellsDendritesSensory Receptor CellsBrainGanglia, SpinalAnimals, NewbornBulbar Palsy, ProgressivePatch-Clamp TechniquesGABAergic NeuronsNeural InhibitionMice, Inbred C57BLModels, Neurological