Motor NeuronsMotor Neuron DiseaseNeuronsRibonucleoproteinsHeterogeneous-Nuclear Ribonucleoprotein Group A-BSurvival of Motor Neuron 1 ProteinHeterogeneous-Nuclear Ribonucleoprotein KHeterogeneous-Nuclear RibonucleoproteinsRibonucleoproteins, Small NuclearNeurons, AfferentCell SurvivalHeterogeneous-Nuclear Ribonucleoprotein Group CSurvival of Motor Neuron 2 ProteinMotor CortexSurvival RateEvoked Potentials, MotorAmyotrophic Lateral SclerosisSpinal CordRibonucleoprotein, U1 Small NuclearRNA-Binding ProteinsMuscular Atrophy, SpinalNucleoproteinsSMN Complex ProteinsMotor ActivityRNA, Heterogeneous NuclearRibonucleoprotein, U2 Small NuclearMolecular Sequence DataAxonsHeterogeneous-Nuclear Ribonucleoprotein Group F-HNerve Tissue ProteinsHeterogeneous-Nuclear Ribonucleoprotein LRNAAction PotentialsRNA, Small NuclearHeterogeneous-Nuclear Ribonucleoprotein URNA, MessengerBase SequencesnRNP Core ProteinsDisease-Free SurvivalRNA SplicingTime FactorsCells, CulturedSurvivalMutationHeLa CellsMolecular Motor ProteinsSpliceosomesNerve DegenerationImmunohistochemistryElectric StimulationRNA PrecursorsCell NucleusSynapsesMice, TransgenicNeuromuscular DiseasesGanglia, InvertebrateRibonucleoprotein, U4-U6 Small NuclearSurvival AnalysisAmino Acid SequenceProtein BindingElectrophysiologyInterneuronsVault Ribonucleoprotein ParticlesSynaptic TransmissionHeterogeneous-Nuclear Ribonucleoprotein DGraft SurvivalMovementDendritesDisease Models, AnimalCholinergic NeuronsSuperoxide DismutaseAplysiaHeterogeneous-Nuclear Ribonucleoprotein Group MDopaminergic NeuronsBrainRibonucleoprotein, U5 Small NuclearElectromyographyMice, Inbred C57BLCell LineAnterior Horn CellsNeuromuscular JunctionNucleic Acid ConformationSensory Receptor CellsGanglia, SpinalSignal TransductionTelomeraseAnimals, NewbornBulbar Palsy, ProgressivePatch-Clamp TechniquesNuclear ProteinsGABAergic NeuronsNeural InhibitionAnimals, Genetically ModifiedModels, NeurologicalGreen Fluorescent ProteinsHippocampusCerebral CortexRNA, Small CytoplasmicCytoplasmAutoantigens