Motor NeuronsNeuronsMotor Neuron DiseaseProtein BindingProtein Interaction MappingCell SurvivalSurvival of Motor Neuron 1 ProteinTwo-Hybrid System TechniquesNeurons, AfferentMolecular Sequence DataApoptosisSurvival of Motor Neuron 2 ProteinMotor CortexSurvival RateEvoked Potentials, MotorProtein Structure, TertiaryAmino Acid SequenceSpinal CordAmyotrophic Lateral SclerosisBinding SitesTranscription FactorsCell LineModels, MolecularMuscular Atrophy, SpinalMotor ActivityCaspasesCells, CulturedApoptosis Regulatory ProteinsBase SequenceCaspase 3Protein ConformationAxonsSMN Complex ProteinsTime FactorsSignal TransductionNerve Tissue ProteinsAction PotentialsInhibitor of Apoptosis ProteinsProto-Oncogene Proteins c-bcl-2ImmunohistochemistryDisease-Free SurvivalMice, TransgenicIn Situ Nick-End LabelingCell Line, TumorSurvivalNerve DegenerationMice, Inbred C57BLDNA FragmentationMolecular Motor ProteinsDisease Models, Animalbcl-2-Associated X ProteinElectric StimulationSynapsesMutationNeuromuscular DiseasesSurvival AnalysisGanglia, InvertebrateCell DeathSuperoxide DismutaseMitochondriaElectrophysiologyMice, KnockoutInterneuronsX-Linked Inhibitor of Apoptosis ProteinBlotting, WesternSynaptic TransmissionGraft SurvivalAnimals, NewbornMovementBrainCholinergic NeuronsDose-Response Relationship, DrugRNA, MessengerDopaminergic NeuronsEnzyme ActivationAplysiaCell ProliferationCell DifferentiationApoptosis Inducing FactorMembrane PotentialsRats, Sprague-DawleyAnterior Horn CellsCaspase InhibitorsElectromyographyNeuromuscular JunctionDendritesSensory Receptor CellsCASP8 and FADD-Like Apoptosis Regulating ProteinGanglia, SpinalCaspase 9Tumor Suppressor Protein p53Cell CountPatch-Clamp TechniquesCerebral CortexBulbar Palsy, ProgressiveNeural InhibitionGABAergic NeuronsTumor Cells, CulturedAnimals, Genetically ModifiedModels, Neurological