Trinucleotide Repeat ExpansionTrinucleotide RepeatsFriedreich AtaxiaDNA Repeat ExpansionSpinocerebellar DegenerationsMyotonic DystrophyFragile X SyndromeHuntington DiseaseFragile X Mental Retardation ProteinIron-Binding ProteinsAllelesMutationRepetitive Sequences, Nucleic AcidSpinocerebellar AtaxiasMachado-Joseph DiseaseBase SequenceHeredodegenerative Disorders, Nervous SystemMolecular Sequence DataNerve Tissue ProteinsGenomic InstabilityFrontotemporal DementiaFlap EndonucleasesAnticipation, GeneticMicrosatellite RepeatsDNANucleic Acid ConformationInverted Repeat SequencesMinisatellite RepeatsTandem Repeat SequencesPedigreeCerebellar AtaxiaAge of OnsetIntranuclear Inclusion BodiesChromosome FragilityMuscular Dystrophy, OculopharyngealGenetic Diseases, InbornRNA-Binding ProteinsPolymerase Chain ReactionAmyotrophic Lateral SclerosisTranscription, GeneticPolymorphism, GeneticNeurodegenerative DiseasesNuclear ProteinsRNA, MessengerPhenotypePeptidesDNA PrimersProteinsDNA RepairGenotypeSequence Analysis, DNADNA-Binding ProteinsReceptors, AndrogenModels, GeneticSaccharomyces cerevisiaeOxidative StressMice, TransgenicTranscription FactorsAmino Acid SequenceStress, PhysiologicalGenes, DominantMyoclonic Epilepsies, ProgressiveDNA ReplicationGenome, HumanMutS Homolog 2 ProteinTranscription Factor CHOPGenetic MarkersRepetitive Sequences, Amino AcidHeterozygoteExonsNucleic Acid HeteroduplexesHeat-Shock ProteinsHeat-Shock ResponseGene ExpressionDisease Models, Animal