FructoseFructokinasesMetabolism, Inborn ErrorsFructose Metabolism, Inborn ErrorsFructosephosphatesFructose-1,6-Diphosphatase DeficiencyAdenosineAdenosine TriphosphateAmino Acid Metabolism, Inborn ErrorsGlucoseReceptor, Adenosine A2AReceptor, Adenosine A1Adenosine DeaminaseReceptor, Adenosine A3Adenosine MonophosphateLipid Metabolism, Inborn ErrorsAdenosine KinaseReceptor, Adenosine A2BFructosediphosphatesAdenine NucleotidesEnergy MetabolismNeonatal ScreeningPurine-Pyrimidine Metabolism, Inborn ErrorsReceptors, Adenosine A2Carbohydrate Metabolism, Inborn ErrorsSteroid Metabolism, Inborn ErrorsReceptors, Purinergic P1Adenosine A2 Receptor AgonistsHexosediphosphatesAdenosine A2 Receptor AntagonistsAdenosine A1 Receptor AntagonistsKineticsGuanosine TriphosphateFructose IntoleranceAdenosine A1 Receptor AgonistsUrea Cycle Disorders, InbornBrain Diseases, Metabolic, InbornPurinergic P1 Receptor AntagonistsLiverReceptors, PurinergicAdenosine TriphosphatasesArgininosuccinic AciduriaPhosphofructokinase-1PhosphatesLipid MetabolismGlycolysisHyperammonemiaAdenosine DiphosphateFructose-BisphosphataseXanthinesMagnesiumPurinergic P1 Receptor AgonistsMutationLactatesTheophyllineApyraseGlucose Transporter Type 5Magnetic Resonance SpectroscopyPhenylketonuriasNucleotidesPhosphocreatineCalciumSmith-Lemli-Opitz SyndromeTime FactorsMolecular Sequence DataUridine TriphosphateHydrogen-Ion ConcentrationMetabolismPhosphorus IsotopesAdenosine-5'-(N-ethylcarboxamide)5'-NucleotidasePhosphotransferasesCyclic AMPCarbon IsotopesReceptors, Purinergic P2Cells, CulturedLactic AcidInosinePyruvatesInfant, NewbornRefractive ErrorsDose-Response Relationship, DrugHomogentisate 1,2-DioxygenaseOxygen ConsumptionOxidative PhosphorylationModels, BiologicalRabbitsPyruvate KinaseHomocystinuriaCandidiasis, Chronic MucocutaneousAdenosine A3 Receptor AntagonistsPyruvate Metabolism, Inborn ErrorsMyocardiumRats, Inbred Strainsalpha-GalactosidaseCoformycinFructose-Bisphosphate AldolaseRats, Sprague-DawleyFabry DiseaseErythrocytes