Trinucleotide Repeat ExpansionTrinucleotide RepeatsFriedreich AtaxiaDNA Repeat ExpansionSpinocerebellar DegenerationsMyotonic DystrophyFragile X SyndromeHuntington DiseaseFragile X Mental Retardation ProteinIron-Binding ProteinsAllelesMutationRepetitive Sequences, Nucleic AcidSpinocerebellar AtaxiasBase SequenceMachado-Joseph DiseaseMolecular Sequence DataHeredodegenerative Disorders, Nervous SystemNerve Tissue ProteinsGenomic InstabilityFrontotemporal DementiaFlap EndonucleasesMicrosatellite RepeatsAnticipation, GeneticDNANucleic Acid ConformationInverted Repeat SequencesMinisatellite RepeatsTandem Repeat SequencesPedigreeCerebellar AtaxiaAge of OnsetIntranuclear Inclusion BodiesChromosome FragilityMuscular Dystrophy, OculopharyngealPolymerase Chain ReactionGenetic Diseases, InbornRNA-Binding ProteinsTranscription, GeneticAmyotrophic Lateral SclerosisPolymorphism, GeneticNeurodegenerative DiseasesNuclear ProteinsPhenotypeSequence Analysis, DNARNA, MessengerDNA PrimersProteinsPeptidesDNA RepairGenotypeAmino Acid SequenceModels, GeneticSaccharomyces cerevisiaeDNA-Binding ProteinsReceptors, AndrogenOxidative StressTranscription FactorsMice, TransgenicStress, PhysiologicalDNA ReplicationGenes, DominantGenome, HumanMyoclonic Epilepsies, ProgressiveGenetic MarkersMutS Homolog 2 ProteinTranscription Factor CHOPRepetitive Sequences, Amino AcidExonsHeterozygoteHeat-Shock ProteinsNucleic Acid HeteroduplexesGene ExpressionHeat-Shock ResponseDisease Models, AnimalGene Expression RegulationGenetic Variation