FructoseFructokinasesMetabolism, Inborn ErrorsFructose Metabolism, Inborn ErrorsFructosephosphatesFructose-1,6-Diphosphatase DeficiencyAdenosineAdenosine TriphosphateAmino Acid Metabolism, Inborn ErrorsGlucoseReceptor, Adenosine A2AReceptor, Adenosine A1Adenosine DeaminaseReceptor, Adenosine A3Adenosine MonophosphateLipid Metabolism, Inborn ErrorsAdenosine KinaseReceptor, Adenosine A2BFructosediphosphatesAdenine NucleotidesEnergy MetabolismNeonatal ScreeningPurine-Pyrimidine Metabolism, Inborn ErrorsReceptors, Adenosine A2Carbohydrate Metabolism, Inborn ErrorsSteroid Metabolism, Inborn ErrorsReceptors, Purinergic P1Adenosine A2 Receptor AgonistsHexosediphosphatesAdenosine A2 Receptor AntagonistsKineticsAdenosine A1 Receptor AntagonistsGuanosine TriphosphateFructose IntoleranceAdenosine A1 Receptor AgonistsUrea Cycle Disorders, InbornLiverBrain Diseases, Metabolic, InbornPurinergic P1 Receptor AntagonistsAdenosine TriphosphatasesReceptors, PurinergicArgininosuccinic AciduriaMolecular Sequence DataPhosphatesPhosphofructokinase-1Lipid MetabolismMutationGlycolysisHyperammonemiaAdenosine DiphosphateFructose-BisphosphataseXanthinesMagnesiumLactatesPurinergic P1 Receptor AgonistsTheophyllineMagnetic Resonance SpectroscopyTime FactorsApyraseNucleotidesGlucose Transporter Type 5PhenylketonuriasHydrogen-Ion ConcentrationPhosphocreatineCalciumMetabolismSmith-Lemli-Opitz SyndromePhosphorus IsotopesUridine TriphosphateModels, BiologicalAdenosine-5'-(N-ethylcarboxamide)PhosphotransferasesCarbon Isotopes5'-NucleotidaseCyclic AMPCells, CulturedReceptors, Purinergic P2Amino Acid SequencePyruvatesBase SequenceLactic AcidInfant, NewbornInosineRabbitsDose-Response Relationship, DrugRefractive ErrorsOxygen ConsumptionOxidative PhosphorylationHomogentisate 1,2-DioxygenasePyruvate KinaseEscherichia coliHomocystinuriaCandidiasis, Chronic MucocutaneousCulture MediaAdenosine A3 Receptor AntagonistsPyruvate Metabolism, Inborn ErrorsRats, Inbred StrainsMyocardiumalpha-GalactosidaseFructose-Bisphosphate Aldolase