Trinucleotide RepeatsTrinucleotide Repeat ExpansionNeurodegenerative DiseasesHuntington DiseaseFriedreich AtaxiaFragile X SyndromeSpinocerebellar DegenerationsHeredodegenerative Disorders, Nervous SystemFragile X Mental Retardation ProteinNerve Tissue ProteinsBase SequenceNerve DegenerationMachado-Joseph DiseaseRepetitive Sequences, Nucleic AcidMolecular Sequence DataBrainNeuronsMutationAllelesNucleic Acid ConformationAlzheimer DiseaseParkinson Diseasealpha-SynucleinDNADisease Models, Animaltau ProteinsMicrosatellite RepeatsIron-Binding ProteinsMice, TransgenicAmyotrophic Lateral SclerosisIntranuclear Inclusion BodiesPeptidesGenomic InstabilityTauopathiesNeuroprotective AgentsCerebellar AtaxiaAge of OnsetNuclear ProteinsPedigreeRNA-Binding ProteinsOligonucleotidesPolymerase Chain ReactionAnticipation, GeneticInclusion BodiesPolymorphism, GeneticFlap EndonucleasesMuscular Dystrophy, OculopharyngealAtaxiaSynucleinsPhenotypeChromosome FragilityAmyloid beta-PeptidesPrionsGenetic Diseases, InbornSpinocerebellar AtaxiasMuscular Atrophy, SpinalMicrogliaPrion DiseasesNervous System DiseasesReceptors, AndrogenMinisatellite RepeatsProteostasis DeficienciesGene Knock-In TechniquesNeuronal Ceroid-LipofuscinosesInverted Repeat SequencesCell DeathAmino Acid SequenceRNA, MessengerModels, GeneticSequence Analysis, DNADNA PrimersOxidative StressOligodeoxyribonucleotidesDNA RepairNucleic Acid HeteroduplexesTranscription, GeneticNucleotidesCells, CulturedChromosome Fragile SitesDinucleotide RepeatsGenotypeFrontotemporal DementiaRNAFrontotemporal Lobar DegenerationCell LineParkinsonian DisordersExonsMitochondriaDNA-Binding ProteinsModels, BiologicalModels, MolecularTandem Repeat SequencesHeterozygoteSaccharomyces cerevisiaeLewy Body DiseaseGenetic VariationAutophagyGene Expression RegulationProteinsChromosome Mapping