Trinucleotide Repeat ExpansionTrinucleotide RepeatsFriedreich AtaxiaDNA Repeat ExpansionSpinocerebellar DegenerationsMyotonic DystrophyFragile X SyndromeHuntington DiseaseFragile X Mental Retardation ProteinIron-Binding ProteinsNeurodegenerative DiseasesAllelesMutationRepetitive Sequences, Nucleic AcidSpinocerebellar AtaxiasMachado-Joseph DiseaseHeredodegenerative Disorders, Nervous SystemNerve Tissue ProteinsBase SequenceFrontotemporal DementiaGenomic InstabilityMolecular Sequence DataAnticipation, GeneticFlap EndonucleasesMicrosatellite RepeatsDNANucleic Acid ConformationPedigreeInverted Repeat SequencesIntranuclear Inclusion BodiesAmyotrophic Lateral SclerosisMinisatellite RepeatsCerebellar AtaxiaAge of OnsetTandem Repeat SequencesChromosome FragilityMuscular Dystrophy, OculopharyngealRNA-Binding ProteinsGenetic Diseases, InbornPolymerase Chain ReactionNuclear ProteinsPolymorphism, GeneticPeptidesMice, TransgenicPhenotypeProteinsBrainDisease Models, AnimalDNA RepairSequence Analysis, DNAReceptors, AndrogenModels, GeneticMyoclonic Epilepsies, ProgressiveGenotypeNerve DegenerationDNA PrimersGenes, DominantTranscription, GeneticNeuronsGenome, HumanAtaxiaExonsDNA ReplicationDNA-Binding ProteinsHeterozygoteRepetitive Sequences, Amino AcidRNA, MessengerAmino Acid SequenceSaccharomyces cerevisiaeGenetic MarkersMutS Homolog 2 ProteinNucleic Acid HeteroduplexesFrontotemporal Lobar DegenerationCell LineGene Frequency