Kidney DiseasesPolycystic Kidney DiseasesKidneyPoint MutationMutation, MissenseRenal Insufficiency, ChronicKidney Failure, ChronicPolycystic Kidney, Autosomal DominantMutationGlomerular Filtration RateTRPP Cation ChannelsKidney Diseases, CysticKidney TransplantationFrameshift MutationKidney Function TestsKidney TubulesChronic DiseaseGerm-Line MutationPedigreeCreatininePolycystic Kidney, Autosomal RecessiveAcute Kidney InjuryProteinuriaKidney CortexRenal DialysisBase SequenceMolecular Sequence DataExonsKidney GlomerulusDisease ProgressionNephrologyMutation RateHeterozygoteRisk FactorsDiabetic NephropathiesAlbuminuriaPolymerase Chain ReactionAmino Acid SubstitutionDNA Mutational AnalysisAmino Acid SequenceAllelesKidney NeoplasmsKidney Tubules, ProximalGenotypePolymorphism, Single-Stranded ConformationalCell LineBiological MarkersTime FactorsHomozygotePhenotypeMutagenesis, Site-DirectedCodon, NonsenseSequence Analysis, DNADisease Models, AnimalKidney MedullaCohort StudiesPrevalenceGenes, RecessiveMutagenesisGenes, DominantCystatin CKidney CalculiCystsUromodulinHematinicsDNA PrimersMembrane ProteinsGenetic TestingCiliaNational Institute of Diabetes and Digestive and Kidney Diseases (U.S.)Cardiovascular DiseasesNephrectomyRNA, MessengerAnemiaChromosome MappingHypertensionKidney Tubules, CollectingProtein Structure, TertiarySeverity of Illness IndexSequence DeletionPodocytesTreatment OutcomeRenal InsufficiencyGenetic LinkageRisk AssessmentSequence Homology, Amino AcidHypertension, RenalCloning, MolecularRetrospective StudiesPrognosisGenetic Predisposition to DiseaseGlomerulosclerosis, Focal SegmentalSignal TransductionProspective StudiesSyndromeEscherichia coliFollow-Up StudiesAIDS-Associated NephropathyModels, MolecularRenal Osteodystrophy