Oxidative PhosphorylationPoint MutationMutationMutation, MissenseMitochondriaUncoupling AgentsAdenosine TriphosphatePhosphorylationOxygen ConsumptionSerineGlycolysisMolecular Sequence DataOligomycinsMitochondria, LiverAmino Acid SequenceCell LineProtein-Serine-Threonine KinasesTyrosineMitochondrial DiseasesKineticsDNA, MitochondrialCell RespirationEnzyme ActivationFrameshift MutationOxidative Phosphorylation Coupling FactorsProtein KinasesPhosphoproteinsAdenosine DiphosphateMitochondrial ProteinsEnergy MetabolismElectron TransportDinitrophenolsCells, CulturedMitochondria, MuscleElectron Transport Complex IMitochondria, HeartProtein BindingBase Sequence2,4-DinitrophenolThreoninePhosphoserineGerm-Line MutationProtein-Tyrosine KinasesMutagenesis, Site-DirectedMitochondrial Proton-Translocating ATPasesModels, BiologicalElectron Transport Complex IVAmino Acid SubstitutionMitochondrial ADP, ATP TranslocasesBinding SitesBlotting, WesternAntimycin ASignal TransductionEnzyme InhibitorsTransfectionProtein Structure, TertiaryPedigreeSuccinatesProtein Kinase CAtractylosidePhosphatesMitochondrial MyopathiesGlucoseCarrier ProteinsCalciumTranscription FactorsDNA-Binding ProteinsCarbonyl Cyanide p-TrifluoromethoxyphenylhydrazoneProton-Translocating ATPasesMembrane ProteinsCyclic AMP-Dependent Protein KinasesProto-Oncogene Proteins c-aktRotenoneCell Line, TumorMuscle, SkeletalRecombinant ProteinsPhosphotyrosinePhosphopeptidesProteinsAdenosine TriphosphatasesOxygenProtein Processing, Post-TranslationalGene Expression RegulationReactive Oxygen SpeciesProto-Oncogene ProteinsNADCarbonyl Cyanide m-Chlorophenyl HydrazoneHeLa CellsEscherichia coliTime FactorsPolymerase Chain ReactionTranscription, GeneticDNA Mutational AnalysisSaccharomyces cerevisiaeCitric Acid CycleAdenine Nucleotide Translocator 1Mitogen-Activated Protein KinasesImmunoblottingMutation RateDNA Primers