Liver GlycogenGlycogenGlycogen SynthaseLiverPhosphorylasesPoint MutationGlycogen PhosphorylaseGlycogen Storage DiseaseGlycogen Synthase Kinase 3Mutation, MissenseGlycogen Phosphorylase, Liver FormMutationLiver DiseasesGlucoseGlycogen Storage Disease Type VIBlood GlucoseLiver NeoplasmsLiver TransplantationGluconeogenesisGlycogen Synthase KinasesLactatesFrameshift MutationGlucosephosphatesPhosphorylase aGlucose-6-PhosphateLiver CirrhosisUridine Diphosphate GlucoseFastingGlycogen-Synthase-D PhosphataseGerm-Line MutationGlucagonMicrosomes, LiverRats, Inbred StrainsLiver RegenerationFatty LiverPhosphorylase KinaseStarvationMusclesInsulinKineticsPedigreeLactic AcidRenal AminoaciduriasBase SequenceMuscle, SkeletalGlucokinaseMolecular Sequence DataFatty Acids, NonesterifiedRats, WistarDietary CarbohydratesAdenosine MonophosphateMutation RateFructoseMitochondria, LiverLiver Function TestsAmino Acid SequenceExonsGlycogen Debranching Enzyme SystemHypoglycemiaLipid MetabolismHeterozygotePortal VeinTime FactorsGlycogen Storage Disease Type IPolymerase Chain ReactionAmino Acid SubstitutionDrug-Induced Liver InjuryGlucosyltransferasesGlucose-6-PhosphataseDiabetes Mellitus, Experimental3-Hydroxybutyric AcidHydroxybutyratesRabbitsPhosphorylationOrgan SizeKetone BodiesGlycolysisCarbohydrate MetabolismDNA Mutational AnalysisPhysical Conditioning, AnimalAllelesAlanineCarbon RadioisotopesEatingMutagenesis, Site-DirectedPhysical ExertionPyruvatesEnzyme ActivationPolymorphism, Single-Stranded ConformationalLiver CirculationLiver Neoplasms, ExperimentalHyperglycemiaHomozygoteCarbon IsotopesBody WeightMutagenesisLiver ExtractsCell LineRats, Sprague-DawleyCodon, Nonsense