Trinucleotide Repeat ExpansionTrinucleotide RepeatsFriedreich AtaxiaIron-Binding ProteinsDNA Repeat ExpansionSpinocerebellar DegenerationsMyotonic DystrophyIronFragile X SyndromeHuntington DiseaseFragile X Mental Retardation ProteinAllelesDexrazoxaneAnemia, SideroblasticIron-Sulfur ProteinsMitochondriaMutationAconitate HydrataseRepetitive Sequences, Nucleic AcidPhosphotransferases (Alcohol Group Acceptor)Iron Chelating AgentsSpinocerebellar AtaxiasMachado-Joseph DiseaseHeredodegenerative Disorders, Nervous SystemMolecular Sequence DataSaccharomyces cerevisiaeBase SequenceMitochondrial ProteinsNerve Tissue ProteinsGenomic InstabilityFerrochelataseFrontotemporal DementiaFlap EndonucleasesSaccharomyces cerevisiae ProteinsAnticipation, GeneticMicrosatellite RepeatsDNAIron-Regulatory ProteinsCation Transport ProteinsNucleic Acid ConformationInverted Repeat SequencesHemeMinisatellite RepeatsTandem Repeat SequencesPedigreeCerebellar AtaxiaUroporphyrinogen III SynthetaseAge of OnsetIntranuclear Inclusion BodiesChromosome FragilityMuscular Dystrophy, OculopharyngealPolymerase Chain ReactionRNA-Binding ProteinsGenetic Diseases, InbornHomeostasisCoproporphyrinogen OxidaseIron OverloadAmyotrophic Lateral SclerosisPolymorphism, GeneticIron, DietaryNeurodegenerative DiseasesPhenotypeNuclear ProteinsRNA, MessengerCytosolPeptidesProteinsDNA RepairOxidative StressGene ExpressionSequence Analysis, DNAMice, TransgenicReceptors, AndrogenModels, GeneticBiological TransportDNA PrimersGenotypeAmino Acid SequenceHeterozygoteTranscription, GeneticGenes, DominantDNA ReplicationMyoclonic Epilepsies, ProgressiveDisease Models, AnimalGenome, HumanMutS Homolog 2 ProteinGenetic MarkersRepetitive Sequences, Amino AcidGene DeletionExonsFungal ProteinsNucleic Acid HeteroduplexesATP-Binding Cassette TransportersIron IsotopesDNA-Binding ProteinsCell LineIron Radioisotopes