CystineSulfurMitochondriaGlutathioneGlutathione TransferaseMitochondria, LiverAmino AcidsSulfur CompoundsCystinosisSequence Homology, Amino AcidAmino Acids, SulfurGlutathione PeroxidaseGlutathione ReductaseGlutathione DisulfideAmino Acid SequenceMitochondria, HeartSulfur IsotopesCysteineOxidation-ReductionCloning, MolecularMolecular Sequence DataCystine Knot MotifsSulfur DioxideAmino Acid SubstitutionMitochondria, MuscleAmino Acid Transport System y+KineticsGlutathione SynthaseBase SequenceMitochondrial ProteinsSulfhydryl CompoundsAmino Acids, EssentialMethionineButhionine SulfoximineMutationCysteamineSequence AlignmentBiological TransportOxidative StressAmino Acid Transport SystemsCystinuriaEscherichia coliBinding SitesSulfidesLiverRecombinant ProteinsModels, MolecularSubstrate SpecificityMitochondrial SwellingAmino Acid MotifsDisulfidesGlutamate-Cysteine LigaseCell LineProtein BindingProtein ConformationMustard GasIntracellular MembranesMutagenesis, Site-DirectedDNA, ComplementaryOxidative PhosphorylationCarrier ProteinsMitochondrial MembranesSaccharomyces cerevisiaeReactive Oxygen SpeciesGlutathione S-Transferase piMolecular WeightProteinsAmino Acid Transport Systems, BasicThiosulfatesChromatography, High Pressure LiquidOxygen ConsumptionProtein Structure, TertiaryRecombinant Fusion ProteinsPeptide FragmentsAntioxidantsAdenosine TriphosphatePhylogenyStructure-Activity RelationshipElectrophoresis, Polyacrylamide GelCattleMaleatesRNA, MessengerLeucineCytosolSequence Homology, Nucleic AcidSulfatesCells, CulturedBacterial ProteinsCell RespirationDNA, MitochondrialDNAPeptidesOxidoreductasesHydrogen-Ion ConcentrationSulfur OxidesMembrane ProteinsHydrogen PeroxideCytochromes cMembrane Potential, MitochondrialAmino Acids, Branched-Chain