PhenylalaninePhenylalanine HydroxylasePhenylalanine Ammonia-LyasePhenylketonuriasEnergy MetabolismLipid MetabolismPhenylpyruvic AcidsTyrosineAmino AcidsKineticsAmmonia-LyasesLiverMolecular Sequence DataPrephenate DehydrataseMetabolismBiopterinLeucineGlucoseAmino Acid SequencePterinsCarbon IsotopesTryptophanOxidation-ReductionMutationHydroxylationAmino Acids, AromaticFencloninePhenylalanine-tRNA LigasePhenylketonuria, Maternalp-FluorophenylalanineMutagenesis, Site-DirectedChromatography, High Pressure LiquidBase SequenceBinding SitesChorismate MutaseEscherichia coliBiotransformationAmino Acids, EssentialCytochrome P-450 Enzyme SystemInsulinMetabolic Networks and PathwaysMagnetic Resonance SpectroscopyCarbon RadioisotopesNutritional RequirementsMicrosomes, LiverHydro-LyasesSubstrate SpecificityPteridinesNitrogenAspartameDeuterium3-Deoxy-7-Phosphoheptulonate SynthaseAlanineModels, BiologicalPhenylacetatesGlycolysisStructure-Activity RelationshipMethionineModels, MolecularIsoleucineRhodotorulaProtein BindingTime FactorsAnabaena variabilisCarbon DioxideMuscle ProteinsOxygen ConsumptionRecombinant ProteinsFatty AcidsBiological TransportHydrogen-Ion ConcentrationLactatesRats, Inbred StrainsMetabolism, Inborn ErrorsDietary ProteinsAmino Acid SubstitutionMuscle, SkeletalAldehyde-LyasesCell LineCarbonCells, CulturedValineDietProtein ConformationLactic AcidStereoisomerismBlood GlucoseRNA, MessengerProtein BiosynthesisPhosphorylationFood, FormulatedGas Chromatography-Mass SpectrometryBrainAcetatesCulture MediaSignal TransductionAmino Acids, Branched-ChainLysineCloning, MolecularBacterial Proteins