Pyruvate Dehydrogenase ComplexDihydrolipoyllysine-Residue AcetyltransferasePyruvate Dehydrogenase (Lipoamide)Pyruvate Dehydrogenase Complex Deficiency DiseaseKetoglutarate Dehydrogenase ComplexDihydrolipoamide DehydrogenasePyruvate Dehydrogenase (Lipoamide)-PhosphataseKetone OxidoreductasesThiamine PyrophosphateThioctic AcidPyruvic AcidPyruvatesDichloroacetic AcidAcetyltransferases3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)Pyruvate DecarboxylaseAzotobacterAcetyl Coenzyme APyruvate KinaseLiver Cirrhosis, BiliaryAurothioglucosePyruvate OxidaseStarvationGeobacillus stearothermophilusKeto AcidsNADMultienzyme ComplexesAcetoinKineticsAcetylcarnitineEscherichia coliL-Lactate DehydrogenaseMolecular Sequence DataDecarboxylationCoenzyme AAmino Acid SequenceCitric Acid CycleMitochondriaAzotobacter vinelandiiProtein KinasesAcidosis, LacticGlucoseMalate DehydrogenaseOxidation-ReductionAlcohol DehydrogenaseGlyceraldehyde-3-Phosphate DehydrogenasesKetoglutaric AcidsGlycolysisSuccinate DehydrogenaseBinding SitesMitochondria, HeartMalatesIsocitrate DehydrogenaseCitrate (si)-SynthaseCattleMyocardiumProtein-Serine-Threonine KinasesLactic AcidMitochondria, LiverElectrophoresis, Polyacrylamide GelChemistryChemical PhenomenaGlutamate DehydrogenaseAcetatesCloning, MolecularIsoenzymesPyruvate SynthaseBase SequenceCarnitineLiverGlucosephosphate DehydrogenaseAldehyde DehydrogenaseMolecular WeightLactatesChromatography, GelAdenosine TriphosphatePhosphorous AcidsEnzyme ActivationProtein ConformationAscaris suumMacromolecular SubstancesEthylmaleimideAcetaldehydeAcyltransferasesAerobiosisGlycine Decarboxylase ComplexRats, Inbred StrainsSequence Homology, Amino AcidSwineMitochondria, MuscleGene Expression Regulation, EnzymologicAlcohol OxidoreductasesMutationMaple Syrup Urine DiseaseThiamineAcetylationPhosphorylationCarbohydrate MetabolismFlavin-Adenine DinucleotideOxygen Consumption