Motor NeuronsMotor Neuron DiseaseNeuronsSurvival of Motor Neuron 1 ProteinNeurons, AfferentCell SurvivalSurvival of Motor Neuron 2 ProteinMotor CortexSurvival RateEvoked Potentials, MotorSpinal CordAmyotrophic Lateral SclerosisMuscular Atrophy, SpinalMotor ActivityAxonsSMN Complex ProteinsRNA, MessengerAction PotentialsNerve Tissue ProteinsDisease-Free SurvivalTime FactorsCells, CulturedSurvivalMolecular Motor ProteinsNerve DegenerationElectric StimulationSynapsesImmunohistochemistryNeuromuscular DiseasesGanglia, InvertebrateMice, TransgenicSurvival AnalysisElectrophysiologyInterneuronsSynaptic TransmissionGraft SurvivalMovementSuperoxide DismutaseCholinergic NeuronsMutationDisease Models, AnimalAplysiaBrainDopaminergic NeuronsDendritesNeuromuscular JunctionElectromyographyAnterior Horn CellsMice, Inbred C57BLAnimals, NewbornSensory Receptor CellsGanglia, SpinalMolecular Sequence DataPatch-Clamp TechniquesBulbar Palsy, ProgressiveGABAergic NeuronsNeural InhibitionModels, NeurologicalSignal TransductionCerebral CortexAnimals, Genetically ModifiedHippocampusRNA-Binding ProteinsFacial NerveGene Expression Regulation, DevelopmentalMembrane PotentialsMotor Skills DisordersCell DifferentiationNeuropeptidesBase SequenceMice, Knockoutgamma-Aminobutyric AcidCell CountBrain StemRats, Sprague-DawleyGene Expression RegulationGreen Fluorescent ProteinsAxonal TransportTreatment OutcomeCentral Nervous SystemAnalysis of VarianceNeurofilament ProteinsCholine O-AcetyltransferaseNerve Growth FactorsIn Situ HybridizationGangliaBehavior, AnimalNeural ConductionMuscle, SkeletalApoptosisCell DeathGrasshoppersLocomotionNerve NetNeurons, EfferentNeuronal PlasticityChick EmbryoReaction TimeRats, WistarExcitatory Postsynaptic Potentials