alpha 1-Antitrypsin Deficiencyalpha 1-AntitrypsinPulmonary EmphysemaEmphysemaLiver DiseasesPhenotypeLiverPulmonary Disease, Chronic ObstructiveLiver CirrhosisForced Expiratory VolumeTrypsin Inhibitorsalpha 1-AntichymotrypsinLiver TransplantationLung DiseasesLungAirway ObstructionPancreatic ElastaseAirway RemodelingHeterozygoteHomozygoteProteostasis DeficienciesBronchiectasisHepatitisLiver NeoplasmsAirway ResistanceAllelesSmokingMutationRespiratory Function TestsSerpinsSpirometryGenotypeBronchitisVital Capacity