Pyruvate Dehydrogenase ComplexDihydrolipoamide DehydrogenasePyruvate Dehydrogenase (Lipoamide)Dihydrolipoyllysine-Residue AcetyltransferaseKetoglutarate Dehydrogenase ComplexPyruvate Dehydrogenase Complex Deficiency DiseasePyruvate Dehydrogenase (Lipoamide)-PhosphataseKetone OxidoreductasesThioctic AcidThiamine Pyrophosphate3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)Pyruvic AcidPyruvatesAcetyltransferasesDichloroacetic AcidPyruvate DecarboxylaseAzotobacterAcetyl Coenzyme ANADPyruvate KinaseLiver Cirrhosis, BiliaryAurothioglucosePyruvate OxidaseMultienzyme ComplexesStarvationGeobacillus stearothermophilusKineticsKeto AcidsEscherichia coliAcetoinAzotobacter vinelandiiAcetylcarnitineMolecular Sequence DataAmino Acid SequenceGlycine Decarboxylase ComplexL-Lactate DehydrogenaseCitric Acid CycleDecarboxylationMitochondriaCoenzyme AOxidation-ReductionGlycine Dehydrogenase (Decarboxylating)Protein KinasesAcidosis, LacticGlucoseBinding SitesMalate DehydrogenaseMyocardiumAlcohol DehydrogenaseGlyceraldehyde-3-Phosphate DehydrogenasesKetoglutaric AcidsGlycolysisSuccinate DehydrogenaseMitochondria, HeartMalatesIsocitrate DehydrogenaseElectrophoresis, Polyacrylamide GelCloning, MolecularCitrate (si)-SynthaseCattleProtein-Serine-Threonine KinasesLactic AcidFlavin-Adenine DinucleotideBase SequenceMitochondria, LiverChemistrySwineChemical PhenomenaGlutamate DehydrogenaseAcetatesMolecular WeightChromatography, GelProtein ConformationIsoenzymesPyruvate SynthaseCarnitineLiverGlucosephosphate DehydrogenaseAldehyde DehydrogenaseLactatesAdenosine TriphosphatePhosphorous AcidsEnzyme ActivationAscaris suumMacromolecular SubstancesEthylmaleimideAcetaldehydeAcyltransferasesMutationAerobiosisProtein BindingOxidoreductasesRats, Inbred StrainsSequence Homology, Amino AcidOxygen ConsumptionMitochondria, MuscleGene Expression Regulation, EnzymologicAlcohol OxidoreductasesMaple Syrup Urine DiseaseSubstrate Specificity