Polycystic Kidney DiseasesPolycystic Kidney, Autosomal DominantPolycystic Kidney, Autosomal RecessiveGenes, RecessiveTRPP Cation ChannelsPolycystic Ovary SyndromeKidneyCystsConsanguinityPedigreeIncidenceCiliaMutationKidney Diseases, CysticKidney TubulesHomozygoteCaroli DiseaseKidney DiseasesPhenotypeGenetic LinkageHyperandrogenismDNA Mutational AnalysisKidney TransplantationSyndromeChromosomes, Human, Pair 16Kidney Failure, ChronicChromosome MappingLiver DiseasesDisease Models, AnimalHeterozygoteMolecular Sequence DataAbnormalities, MultipleMutation, MissenseHirsutismLod ScoreCyst FluidRats, Mutant StrainsGenes, DominantOrofaciodigital SyndromesExonsProteinsBase SequenceRetinitis PigmentosaKidney Tubules, CollectingFrameshift MutationOligomenorrheaKidney CortexGenotypeMembrane ProteinsDisease ProgressionMicrocephalyCodon, NonsenseKidney Function TestsAmino Acid SequenceAllelesHaplotypesGenetic MarkersMice, Mutant StrainsInfant, NewbornCiliary Motility DisordersIchthyosisAnovulationKidney Tubules, ProximalGenetic TestingHypotrichosisRisk FactorsGlomerular Filtration RateOrgan SizeEpithelial CellsAge of OnsetKidney NeoplasmsKidney CalculiTime FactorsMetforminPregnancyFamily HealthRetrospective StudiesAcute Kidney InjuryKidney GlomerulusReceptors, VasopressinIchthyosiform Erythroderma, CongenitalPolymerase Chain ReactionCell LineDogsHematuriaPolymorphism, Single-Stranded ConformationalNephronsReceptors, Cell SurfaceClomiphenePakistanIntellectual DisabilityPolymorphism, GeneticHypertension, RenalIothalamic AcidRNA, MessengerMulticystic Dysplastic KidneyNephrectomyTreatment OutcomeOvaryMice, Knockout