Congenital HyperinsulinismHyperinsulinismSulfonylurea ReceptorsReceptors, DrugPotassium Channels, Inwardly RectifyingDiazoxideHypoglycemiaDiagnostic Techniques, EndocrineHyperammonemiaGlutamate DehydrogenaseATP-Binding Cassette TransportersPancreatectomyInsulinInsulinomaKATP ChannelsInsulin AntibodiesSulfonylurea CompoundsBeckwith-Wiedemann Syndrome3-Hydroxyacyl CoA DehydrogenasesPotassium ChannelsInfant, NewbornCongenital Disorders of GlycosylationCyclin-Dependent Kinase Inhibitor p57MutationChromosomes, Human, Pair 11Islets of LangerhansTolbutamideInsulin-Secreting CellsHyperandrogenismBlood GlucoseMutation, MissenseChlorthalidoneOctreotideProinsulinPancreasHamartomaC-PeptideHeterozygoteMosaicismPancreatic NeoplasmsHypopituitarismPedigreeAmmoniaSeizuresGenes, DominantSyndromeAdenosine TriphosphateGlucoseHomozygoteGlucose Tolerance TestPoint Mutation