Huntington DiseaseTrinucleotide Repeat ExpansionTrinucleotide RepeatsChromosomes, Human, Pair 4Nerve Tissue ProteinsQuinolinic AcidNuclear ProteinsCorpus Striatum3-Hydroxyanthranilate 3,4-DioxygenaseAge of OnsetChoreaProdromal SymptomsRats, TransgenicDisease Models, AnimalWitchcraftNeurodegenerative DiseasesCaudate NucleusGenetic TestingMice, TransgenicRotarod Performance TestAtrophyBrainNeostriatumTetrabenazineMythologyQuinolinic AcidsMutationPeptidesNerve Fibers, UnmyelinatedNeuronsInclusion BodiesPutamenDopamine and cAMP-Regulated Phosphoprotein 32Mutant ProteinsPedigreeChromosome BandingLipoylationGene Knock-In TechniquesGenetic MarkersPhenotypeAllelesDisease ProgressionGenetic CounselingGenetic LinkageNitro CompoundsEarly DiagnosisHeterozygote DetectionMagnetic Resonance ImagingGenotypeCognition DisordersNerve DegenerationChromosome MappingAutophagy