Frontotemporal Lobar DegenerationFrontotemporal DementiaTDP-43 ProteinopathiesDementiaInclusion BodiesPick Disease of the BrainRNA-Binding Protein FUSAmyotrophic Lateral SclerosisAtrophyDNA Repeat Expansiontau ProteinsAphasia, Primary ProgressiveIntercellular Signaling Peptides and ProteinsFrontal LobeNeuropsychological TestsBrainAphasia, BrocaDNA-Binding ProteinsAlzheimer DiseaseTauopathiesMotor Neuron DiseaseTemporal LobePrimary Progressive Nonfluent AphasiaSupranuclear Palsy, ProgressiveNeurodegenerative DiseasesNerve DegenerationUbiquitinAutopsyMagnetic Resonance ImagingIntranuclear Inclusion BodiesMutationNeurofibrillary TanglesAphasiaAge of OnsetApraxiasProsopagnosiaRetinal DegenerationMacular DegenerationSclerosisImage Processing, Computer-AssistedMental Status ScheduleNeuroimagingNeuronsLanguage TestsLewy Body DiseaseCognition DisordersCerebral CortexDisease ProgressionGenetic Predisposition to DiseaseDNA Mutational AnalysisNerve Tissue ProteinsMutation, MissenseWallerian DegenerationHippocampusMotor NeuronsBrain MappingPedigreeSpinal CordHEK293 CellsImmunohistochemistryCase-Control StudiesPhenotypeGenotypeProteinsCohort StudiesDisease Models, AnimalCytoplasm