Lysosomal Storage DiseasesLysosomal Storage Diseases, Nervous Systemalpha-MannosidosisMucopolysaccharidosis VIIGlycogen Storage Disease Type ILysosomesGaucher DiseaseFucosidosisGlycogen Storage DiseaseMucopolysaccharidosis IGlycogen Storage Disease Type IIAspartylglucosaminuriaMucolipidosesEnzyme Replacement TherapySphingolipidosesMucopolysaccharidosis IIIAspartylglucosylaminaseLeukodystrophy, MetachromaticCerebroside-SulfataseIduronidaseSandhoff DiseaseGangliosidosis, GM1Cholesterol Ester Storage DiseaseGangliosidoses, GM2GlucosylceramidaseMucopolysaccharidosis VIalpha-GalactosidaseNeuronal Ceroid-LipofuscinosesMetabolism, Inborn ErrorsGlycogen Storage Disease Type IVGlycogen Storage Disease Type IIIMucopolysaccharidosesFabry Diseasealpha-GlucosidasesGlucuronidaseN-Acetylgalactosamine-4-SulfataseNiemann-Pick DiseasesMucopolysaccharidosis IVbeta-N-Acetylhexosaminidasesbeta-MannosidosisPlant PoisoningTay-Sachs DiseaseHexosaminidase BMalvaceaeWolman DiseaseGenetic TherapyG(M2) Gangliosidealpha-MannosidaseGangliosidosesSialic Acid Storage DiseaseLeukodystrophy, Globoid Cellbeta-GlucosidaseSerine ProteasesChondro-4-SulfataseDependovirusCystinosisGlycogen Storage Disease Type VIIPsychosineDisease Models, AnimalHexosaminidase AMannosephosphatesGenetic VectorsGlucosylceramidesGlycosaminoglycansMultiple Sulfatase Deficiency DiseaseNiemann-Pick Disease, Type CLiverTransient Receptor Potential ChannelsFibroblastsMucopolysaccharidosis IIMannosidasesBrainDipeptidyl-Peptidases and Tripeptidyl-PeptidasesMutationGlycosphingolipidsGlucose-6-PhosphataseMice, KnockoutCentral Nervous SystemTRPM Cation ChannelsAutophagyPhenotypeAcetylglucosaminidaseSphingomyelin PhosphodiesteraseGlycogen Storage Disease Type VMice, Mutant StrainsCat DiseasesLipid Metabolism, Inborn ErrorsMolecular Sequence DataGlycogen Debranching Enzyme SystemCarbohydrate Metabolism, Inborn ErrorsHydrolasesDrug StorageGlycogen Storage Disease Type VI1-DeoxynojirimycinIduronate SulfataseLipidosesImino Sugarsbeta-MannosidaseGene Transfer Techniquesbeta-Galactosidase