Motor NeuronsEndocytosisNeuronsMotor Neuron DiseaseSurvival of Motor Neuron 1 ProteinNeurons, AfferentCell SurvivalSurvival of Motor Neuron 2 ProteinMotor CortexSurvival RateEvoked Potentials, MotorSpinal CordAmyotrophic Lateral SclerosisClathrinMuscular Atrophy, SpinalMotor ActivityAxonsNerve Tissue ProteinsSMN Complex ProteinsDynaminsCells, CulturedAction PotentialsTime FactorsDisease-Free SurvivalSynapsesSurvivalElectric StimulationMolecular Motor ProteinsMutationImmunohistochemistryNerve DegenerationSignal TransductionEndosomesMice, TransgenicNeuromuscular DiseasesSynaptic TransmissionGanglia, InvertebrateClathrin-Coated VesiclesElectrophysiologySurvival AnalysisInterneuronsDynamin ICoated Pits, Cell-MembraneGreen Fluorescent ProteinsNeuromuscular JunctionGraft SurvivalMovementSuperoxide DismutaseDisease Models, AnimalCholinergic NeuronsDopaminergic NeuronsMice, Inbred C57BLBrainPatch-Clamp TechniquesCell LineAplysiaProtein TransportDendritesAnimals, NewbornCell MembraneElectromyographySensory Receptor CellsAnterior Horn CellsGanglia, SpinalHippocampusNeural InhibitionAdaptor Protein Complex 2Animals, Genetically ModifiedModels, NeurologicalMolecular Sequence DataBulbar Palsy, ProgressiveGABAergic NeuronsDynamin IIMice, KnockoutCerebral CortexMembrane PotentialsNeuropeptidesRats, Sprague-DawleyModels, BiologicalFacial NerveBrain StemTransferrinMicroscopy, FluorescenceMotor Skills DisordersSynaptic VesiclesCell DifferentiationAxonal Transportgamma-Aminobutyric AcidCell CountMicroscopy, ConfocalAmino Acid Sequencerab5 GTP-Binding ProteinsMembrane ProteinsGene Expression Regulation, DevelopmentalAnalysis of VarianceCentral Nervous SystemTreatment OutcomeCell DeathApoptosisNeuronal Plasticity