Congenital HyperinsulinismDiazoxideHyperinsulinismSulfonylurea ReceptorsReceptors, DrugPotassium Channels, Inwardly RectifyingHypoglycemiaKATP ChannelsDiagnostic Techniques, EndocrinePotassium ChannelsATP-Binding Cassette TransportersHyperammonemiaDecanoic AcidsHydroxy AcidsPancreatectomyInsulinGlutamate DehydrogenaseTolbutamideInsulinomaSulfonylurea CompoundsIslets of LangerhansInsulin AntibodiesBeckwith-Wiedemann Syndrome3-Hydroxyacyl CoA DehydrogenasesInfant, NewbornCongenital Disorders of GlycosylationAdenosine TriphosphateCyclin-Dependent Kinase Inhibitor p57Insulin-Secreting CellsMutationBlood GlucoseChromosomes, Human, Pair 11PinacidilGlyburideHyperandrogenismProinsulinGlucoseMutation, MissenseChlorthalidonePancreasMitochondria, HeartOctreotideIschemic Preconditioning, MyocardialCromakalimHamartomaHypoglycemic AgentsC-PeptidePotassium RadioisotopesHeterozygoteMaxillary ArteryMosaicismPancreatic NeoplasmsHypopituitarismPicolinesPedigreePotassium Channel BlockersAmmoniaSodium Chloride Symporter InhibitorsSeizuresGenes, DominantMinoxidilSyndromeVasodilator AgentsHomozygoteRubidium RadioisotopesGlucose Tolerance TestPoint MutationInjections, Intravenous