ElastinTropoelastinDesmosineElastic TissueIsodesmosineProteasome Endopeptidase ComplexPancreatic ElastaseProteolysisProtein-Lysine 6-OxidaseUbiquitinBiodegradation, EnvironmentalCollagenLigamentsUbiquitinationMolecular Sequence DataUbiquitin-Protein LigasesAortic Stenosis, SupravalvularCysteine EndopeptidasesCutis LaxaAmino Acid SequenceCells, CulturedAortaExtracellular MatrixRNA, MessengerUbiquitinsMatrix Metalloproteinase 12Cell LineMultienzyme ComplexesFibroblastsEndoplasmic Reticulum-Associated DegradationElasticityWilliams SyndromeKineticsHydrolysisProtein BindingMutationPeptide HydrolasesConnective TissueProtease InhibitorsCattleProtein Processing, Post-TranslationalAminopropionitrileBase SequenceMicrofibrilsTime FactorsExtracellular Matrix ProteinsSignal TransductionCysteine Proteinase InhibitorsRNA StabilityProtein Structure, TertiaryEndopeptidasesModels, BiologicalAmino AcidsEndoplasmic ReticulumBlotting, WesternElastomersProteasome InhibitorsSubstrate SpecificityLungF-Box ProteinsRecombinant ProteinsMatrix Metalloproteinase 9AutophagyMetalloendopeptidasesProteinsCathepsinsGene Expression RegulationAorta, AbdominalPhosphorylation