Pyruvate Dehydrogenase ComplexDecarboxylationDihydrolipoyllysine-Residue AcetyltransferasePyruvate Dehydrogenase (Lipoamide)Pyruvate Dehydrogenase Complex Deficiency DiseaseKetoglutarate Dehydrogenase ComplexDihydrolipoamide DehydrogenasePyruvate Dehydrogenase (Lipoamide)-PhosphataseKetone OxidoreductasesThiamine PyrophosphateThioctic AcidPyruvic AcidPyruvatesDichloroacetic AcidPyruvate DecarboxylaseAcetyltransferases3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)Acetyl Coenzyme AAzotobacterPyruvate OxidaseKeto AcidsPyruvate KinaseLiver Cirrhosis, BiliaryAurothioglucoseKineticsStarvationGeobacillus stearothermophilusMultienzyme ComplexesNADAcetoinEscherichia coliAcetylcarnitineMolecular Sequence DataCoenzyme ACitric Acid CycleL-Lactate DehydrogenaseAmino Acid SequenceMitochondriaAzotobacter vinelandiiKetoglutaric AcidsMalate DehydrogenaseOxidation-ReductionProtein KinasesGlucoseCarboxy-LyasesAcidosis, LacticMalatesBinding SitesIsocitrate DehydrogenaseAlcohol DehydrogenaseGlyceraldehyde-3-Phosphate DehydrogenasesPyruvate SynthaseGlycolysisSuccinate DehydrogenaseMitochondria, HeartChemistryMitochondria, LiverChemical PhenomenaLactic AcidAcetatesCattleMyocardiumCitrate (si)-SynthaseElectrophoresis, Polyacrylamide GelProtein-Serine-Threonine KinasesCloning, MolecularLiverGlutamate DehydrogenaseBase SequenceIsoenzymesLactatesMolecular WeightCatalysisCarnitineChromatography, GelGlucosephosphate DehydrogenaseProtein ConformationAcetaldehydeAldehyde DehydrogenaseAdenosine TriphosphateEnzyme ActivationThiaminePhosphorous AcidsSubstrate SpecificitySequence Homology, Amino AcidAerobiosisAscaris suumMacromolecular SubstancesMaple Syrup Urine DiseaseRats, Inbred StrainsEthylmaleimideMutationAcyltransferasesMagnetic Resonance SpectroscopyAlcohol OxidoreductasesSwineGene Expression Regulation, EnzymologicGlycine Decarboxylase ComplexMitochondria, MusclePyruvate Carboxylase