Cystic FibrosisFibrosisCystic Fibrosis Transmembrane Conductance RegulatorPseudomonas InfectionsEndomyocardial FibrosisPseudomonas aeruginosaIdiopathic Pulmonary FibrosisSweatLiver CirrhosisSputumRetroperitoneal FibrosisMice, Inbred CFTRLungBurkholderia InfectionsBurkholderia cepaciaChloridesExocrine Pancreatic InsufficiencyBleomycinChloride ChannelsRespiratory MucosaTobramycinNasal MucosaForced Expiratory VolumePancreatinNeonatal ScreeningOral Submucous FibrosisRespiratory Function TestsBurkholderia cepacia complexBronchiectasisLiver Cirrhosis, ExperimentalEpithelial CellsLung DiseasesRespiratory SystemPancreatic ExtractsMutationDisease Models, AnimalHydroxyprolineLung TransplantationBronchiMucusHepatic Stellate CellsAnti-Bacterial AgentsUreteral ObstructionHeterozygote DetectionExpectorantsMeconiumMyofibroblastsAlginatesTransforming Growth Factor betaCollagenCarbon TetrachloridePancrelipaseTracheaFibroblastsPeritoneal FibrosisMice, Inbred C57BLAchromobacter denitrificansBiopsyCells, CulturedMucociliary ClearancePhenotypeBurkholderia cenocepaciaSweat GlandsCollagen Type IIILiverVital CapacityCell LineCollagen Type IAspergillosis, Allergic BronchopulmonaryAminophenolsLeukocyte ElastaseBronchoalveolar Lavage FluidIon TransportGenotypeDisease ProgressionChronic DiseaseEpitheliumTime FactorsAdministration, InhalationRNA, MessengerRespiratory Tract InfectionsBiological MarkersAmilorideKidneyGenetic TestingMice, KnockoutSeverity of Illness IndexHexuronic AcidsInflammationColistinStenotrophomonas maltophiliaGlucuronic AcidMolecular Sequence DataMyocardiumNephritis, InterstitialScleroderma, SystemicExocrine GlandsMucinsPolymerase Chain ReactionMembrane Proteins