Pyruvate CarboxylaseAcetyl-CoA CarboxylasePyruvate Carboxylase Deficiency DiseasePyruvatesBiotinPyruvate KinasePhosphoenolpyruvate CarboxylaseRibulose-Bisphosphate CarboxylasePyruvate Dehydrogenase ComplexPyruvic AcidAcetyl Coenzyme AOxaloacetatesCarbon-Carbon LigasesOxaloacetic AcidMethylmalonyl-CoA DecarboxylaseAvidinLigasesCarbon-Nitrogen LigasesRhizobium etliCarboxyl and Carbamoyl TransferasesCarboxy-LyasesGluconeogenesisMalatesCitric Acid CyclePyruvate DecarboxylaseCitratesGlucoseLiverMalate DehydrogenaseKineticsCoenzyme APhosphoenolpyruvate Carboxykinase (GTP)LactatesPyruvate OxidasePhosphoenolpyruvateCarbon DioxideMitochondria, LiverPyruvate Dehydrogenase (Lipoamide)Aspartic AcidCarbon IsotopesMolecular Sequence DataAdenosine TriphosphateBicarbonatesKetoglutaric AcidsApoenzymesMagnesiumTricarboxylic AcidsAcetatesLactic AcidCitric AcidAcetoacetatesDicarboxylic AcidsOxamic AcidAmino Acid SequenceModels, BiologicalStarvationSuccinic AcidAdenosine DiphosphateMitochondriaCarbonFructose-BisphosphataseCitrate (si)-SynthaseGlycolysisSuccinatesPyruvate Dehydrogenase (Lipoamide)-PhosphataseGlutamineRibulosephosphatesBinding SitesBase SequenceFormiminoglutamic AcidATP Citrate (pro-S)-LyaseOxidation-ReductionFatty AcidsMacromolecular SubstancesAdipose TissueTrinitrobenzenesulfonic AcidChickensGene Expression Regulation, EnzymologicEnzyme ActivationGluconatesEscherichia coliRats, Inbred StrainsPentosephosphatesAcyl Coenzyme AMagnetic Resonance SpectroscopyCulture MediaKetoglutarate Dehydrogenase ComplexMutationElectrophoresis, Cellulose AcetateVitamin K