Polycystic Kidney DiseasesPolycystic Kidney, Autosomal DominantBile DuctsPolycystic Kidney, Autosomal RecessiveGenes, RecessiveTRPP Cation ChannelsCommon Bile DuctPolycystic Ovary SyndromeBileBile Duct DiseasesBile Acids and SaltsBile Ducts, ExtrahepaticKidneyBile Duct NeoplasmsBile Ducts, IntrahepaticCystsConsanguinityPedigreeCommon Bile Duct DiseasesCiliaMutationKidney Diseases, CysticCholestasisPancreatic DuctsCaroli DiseaseGallstonesAdenoma, Bile DuctKidney TubulesCholangiopancreatography, Endoscopic RetrogradeCommon Bile Duct NeoplasmsCholangiographyHepatic Duct, CommonHomozygoteCholestasis, ExtrahepaticLiver DiseasesKidney DiseasesPhenotypeCystic DuctGenetic LinkageHyperandrogenismDNA Mutational AnalysisSyndromeKidney Tubules, CollectingKidney TransplantationChromosomes, Human, Pair 16Disease Models, AnimalLiverKidney Failure, ChronicCholelithiasisMolecular Sequence DataThoracic DuctCholecystectomy, LaparoscopicChromosome MappingHeterozygoteBiliary TractHirsutismMutation, MissenseAbnormalities, MultipleCyst FluidLod ScoreRats, Mutant StrainsJaundice, ObstructiveGenes, DominantOrofaciodigital SyndromesCholecystectomyCholangitisLigationBiliary Tract Surgical ProceduresProteinsBase SequenceCholedocholithiasisExonsSphincterotomy, EndoscopicKidney CortexGallbladderRetinitis PigmentosaBiliary Tract DiseasesMembrane ProteinsEpithelial CellsFrameshift MutationOligomenorrheaAmino Acid SequenceSalivary DuctsGenotypeDisease ProgressionMicrocephalyCodon, NonsenseKidney Function TestsMice, Mutant StrainsAllelesImmunohistochemistryBile PigmentsBile CanaliculiAmpulla of VaterHaplotypesOrgan SizeCholangiopancreatography, Magnetic ResonanceGenetic MarkersKidney Tubules, ProximalDogs