Huntington DiseaseTrinucleotide Repeat ExpansionTrinucleotide RepeatsChromosomes, Human, Pair 4Nerve Tissue ProteinsQuinolinic AcidNuclear ProteinsCorpus StriatumAge of Onset3-Hydroxyanthranilate 3,4-DioxygenaseDisease Models, AnimalChoreaProdromal SymptomsRats, TransgenicBrainWitchcraftNeurodegenerative DiseasesRotarod Performance TestCaudate NucleusMice, TransgenicNeostriatumGenetic TestingAtrophyTetrabenazineMutationMythologyNeuronsBehavior, AnimalQuinolinic AcidsPeptidesNerve Fibers, UnmyelinatedMotor ActivityPutamenInclusion BodiesPhenotypeDopamine and cAMP-Regulated Phosphoprotein 32Mutant ProteinsPedigreeGene Knock-In TechniquesChromosome BandingLipoylationGenetic MarkersAllelesDisease ProgressionGenetic CounselingMagnetic Resonance ImagingGenetic LinkageNitro CompoundsEarly DiagnosisCognition DisordersHeterozygote DetectionBehavioral SymptomsGenotypeNeuropsychological TestsCerebral CortexNerve DegenerationLongitudinal StudiesAge FactorsChromosome MappingSeverity of Illness IndexFamilyAutophagyPsychomotor PerformanceHeterozygote