Motor NeuronsAmyotrophic Lateral SclerosisMotor Neuron DiseaseNeuronsSurvival of Motor Neuron 1 ProteinSpinal CordSuperoxide DismutaseNeurons, AfferentMotor CortexEvoked Potentials, MotorSurvival of Motor Neuron 2 ProteinMuscular Atrophy, SpinalMotor ActivityAxonsRNA-Binding Protein FUSNerve DegenerationMice, TransgenicSMN Complex ProteinsNerve Tissue ProteinsAction PotentialsAnterior Horn CellsDisease Models, AnimalNeuromuscular DiseasesBulbar Palsy, ProgressiveMutationElectric StimulationDNA Repeat ExpansionMolecular Motor ProteinsSynapsesInclusion BodiesBrainElectromyographyGanglia, InvertebrateNeurofilament ProteinsRiluzoleNeuromuscular JunctionElectrophysiologyCells, CulturedFrontotemporal DementiaSynaptic TransmissionInterneuronsGuamMovementImmunohistochemistryAnimals, Genetically ModifiedAxonal TransportCholinergic NeuronsFrontotemporal Lobar DegenerationAplysiaDopaminergic NeuronsFasciculationTime FactorsDendritesCerebral CortexPatch-Clamp TechniquesModels, NeurologicalSensory Receptor CellsFacial NerveGanglia, SpinalNeural InhibitionGABAergic NeuronsNeurodegenerative DiseasesAstrocytesBrain StemAnimals, NewbornCentral Nervous SystemTDP-43 ProteinopathiesMuscle, SkeletalMice, Inbred C57BLNeural ConductionGlutamic AcidCholine O-AcetyltransferaseMembrane PotentialsHippocampusNeurogliagamma-Aminobutyric AcidParalysisMotor Skills DisordersCell DeathRats, TransgenicGreen Fluorescent ProteinsBehavior, AnimalCell CountNeuroprotective AgentsNeuropeptidesReaction TimeRotarod Performance TestGangliaCell SurvivalGrasshoppersNeurons, EfferentNerve NetLocomotionPsychomotor PerformanceRats, Sprague-DawleyPeripheral NervesPyramidal TractsAnalysis of VarianceMedulla OblongataExcitatory Postsynaptic Potentials