Huntington DiseaseAllelesTrinucleotide Repeat ExpansionTrinucleotide RepeatsChromosomes, Human, Pair 4Nerve Tissue ProteinsQuinolinic AcidNuclear ProteinsCorpus StriatumAge of Onset3-Hydroxyanthranilate 3,4-DioxygenaseChoreaProdromal SymptomsRats, TransgenicDisease Models, AnimalMutationWitchcraftNeurodegenerative DiseasesGenetic TestingMice, TransgenicCaudate NucleusAtrophyRotarod Performance TestBrainNeostriatumTetrabenazineMythologyGenotypeQuinolinic AcidsPhenotypePeptidesGenetic MarkersPedigreeNerve Fibers, UnmyelinatedNeuronsInclusion BodiesPutamenMutant ProteinsGene FrequencyGenetic LinkageChromosome BandingDopamine and cAMP-Regulated Phosphoprotein 32Gene Knock-In TechniquesLipoylationHeterozygoteDisease ProgressionChromosome MappingGenetic CounselingGenetic Predisposition to DiseaseHeterozygote DetectionNitro CompoundsPolymorphism, Restriction Fragment LengthEarly DiagnosisMolecular Sequence DataMagnetic Resonance ImagingCognition DisordersNerve DegenerationGenetic Diseases, InbornAutophagyFamilyLongitudinal Studies