• hypoglycemia
  • If possible, individuals who suspect they might have HFI, should avoid testing via fructose challenge as the results are non-conclusive for individuals with HFI and even if the diagnostic administration fructose is properly controlled, profound hypoglycemia and its sequelae can threaten the patient's well-being. (wikipedia.org)
  • glucose
  • Fructose is replaced in the diet by glucose, maltose or other sugars. (wikipedia.org)
  • Metabolism is usually divided into two categories: catabolism, the breaking down of organic matter for example, the breaking down of glucose to pyruvate, by cellular respiration, and anabolism, the building up of components of cells such as proteins and nucleic acids. (wikipedia.org)
  • Amino acids also contribute to cellular energy metabolism by providing a carbon source for entry into the citric acid cycle (tricarboxylic acid cycle), especially when a primary source of energy, such as glucose, is scarce, or when cells undergo metabolic stress. (wikipedia.org)
  • Glycolysis (from glycose , an older term [ 1 ] for glucose + -lysis degradation) is the metabolic pathway that converts glucose C 6 H 12 O 6 , into pyruvate , CH 3 COCOO − + H + . The free energy released in this process is used to form the high-energy compounds ATP ( adenosine triphosphate ) and NADH ( reduced nicotinamide adenine dinucleotide ). (omicsgroup.org)
  • For simple fermentations , the metabolism of one molecule of glucose to two molecules of pyruvate has a net yield of two molecules of ATP. (omicsgroup.org)
  • liver
  • for example, experiments can show that urea , the chief nitrogen-containing end product of protein metabolism in mammals , is formed exclusively in the liver . (britannica.com)
  • dietary
  • When patients are diagnosed with HFI, a dietary history will often reveal an aversion to fruit and other foods that contain large amounts of fructose. (wikipedia.org)
  • Because of the ease of therapy (dietary exclusion of fructose), HFI can be effectively managed if properly diagnosed. (wikipedia.org)
  • Once identified, parents of infants who carry mutant aldolase B alleles leading to HFI, or older individuals who have clinical histories compatible with HFI can be identified and counselled with regard to preventive therapy: dietary exclusion of foods containing fructose, sucrose, or sorbitol. (wikipedia.org)
  • Stable patients without acute intoxication events are treated by careful dietary planning that avoids fructose and its metabolic precursors. (wikipedia.org)
  • No treatment is indicated for essential fructosuria, while the degree of fructosuria depends on the dietary fructose intake, it does not have any clinical manifestations. (wikipedia.org)
  • common
  • Affected individuals are asymptomatic and healthy, provided they do not ingest foods containing fructose or any of its common precursors, sucrose and sorbitol. (wikipedia.org)