Motor Neuron DiseaseMotor NeuronsNeuromuscular DiseasesBulbar Palsy, ProgressiveAmyotrophic Lateral SclerosisMuscular Atrophy, SpinalNeuronsSurvival of Motor Neuron 1 ProteinSpinal CordSurvival of Motor Neuron 2 ProteinAnterior Horn CellsNerve DegenerationSMN Complex ProteinsSuperoxide DismutaseMuscular Disorders, AtrophicMotor CortexFasciculationBulbo-Spinal Atrophy, X-LinkedGaggingMuscular AtrophyAxonsNeurons, AfferentTDP-43 ProteinopathiesFrontotemporal Lobar DegenerationNeurofilament ProteinsFrontotemporal DementiaElectromyographyToxascariasisbeta-Hexosaminidase beta ChainEvoked Potentials, MotorRNA-Binding Protein FUSPharyngostomyRiluzolePyrrolidonecarboxylic AcidInclusion BodiesNeural ConductionElectric InjuriesDeglutition DisordersPick Disease of the BrainMotor ActivityMice, TransgenicBrain Injury, ChronicLathyrismDEAD Box Protein 20Disease Models, AnimalUlnar NerveMutationNerve Tissue ProteinsSpinal Cord DiseasesBrainPeripheral NervesNeuromuscular JunctionAction PotentialsSandhoff DiseaseMarchiafava-Bignami DiseaseRats, TransgenicNeurologic ExaminationCricoid CartilageAxonal TransportDementiaDNA Repeat ExpansionParalysisSpinal Muscular Atrophies of ChildhoodRecruitment, NeurophysiologicalElectric StimulationMuscle, SkeletalAge of OnsetAnimals, Genetically ModifiedSpastic Paraplegia, HereditaryMusclesGastrostomyMuscle WeaknessImmunohistochemistrySpinal Nerve RootsCells, CulturedCell DeathTime FactorsMolecular Motor ProteinsMice, Inbred C57BLPedigreeCell CountSynapsesThyrotropin-Releasing HormonePhenotypeGanglia, InvertebrateNervous System DiseasesAtrophyNeuroprotective AgentsNeuroimaging