ElastinElastic TissueMarfan SyndromeMicrofibrilsMicrofilament ProteinsTropoelastinElasticityEctopia LentisDesmosineLigamentsElastic ModulusExtracellular Matrix ProteinsIsodesmosineConnective TissueLatent TGF-beta Binding ProteinsExtracellular MatrixContractile ProteinsProtein-Lysine 6-OxidaseCollagenPancreatic ElastaseFibroblastsMicroscopy, ElectronSkin AbnormalitiesActin CytoskeletonCutis LaxaStress, MechanicalSkinAortic Stenosis, SupravalvularAortaBiomechanical PhenomenaDermisCardiovascular AbnormalitiesCells, CulturedChromosomes, Human, Pair 15ForeskinCattleMolecular Sequence DataSolanaceaeCiliary BodyFluorescent Antibody TechniqueTensile StrengthElastomersMatrix Metalloproteinase 12Scleroderma, SystemicComplianceAminopropionitrileWilliams SyndromeMicroscopy, ImmunoelectronPhenotypeConnective Tissue DiseasesAmino Acid SequenceLens Capsule, CrystallineBase SequenceArteriesElastic CartilageImmunohistochemistryViscosityRNA, MessengerFluorescent Antibody Technique, IndirectExonsAorta, AbdominalMuscle, Smooth, VascularLungMitral Valve ProlapseMutationDecorinProlineConnectinAorta, ThoracicCalcium-Binding ProteinsChromosomes, Human, Pair 5Transforming Growth Factor betaModels, BiologicalMicroscopy, Electron, ScanningRecombinant Proteins