Protein ConformationHeavy Chain DiseaseMetallochaperonesCation Transport ProteinsMachado-Joseph DiseaseCopperHepatolenticular DegenerationProtein BindingMolecular ConformationHeredodegenerative Disorders, Nervous SystemProtein FoldingAmino Acid SequenceAdenosine TriphosphatasesMolecular Sequence DataProtein Structure, TertiaryModels, MolecularBinding SitesPeptidesProtein Structure, SecondaryMenkes Kinky Hair SyndromeProteinsCircular DichroismMutationNerve Tissue ProteinsThermodynamicsDeuterium Exchange MeasurementImmunoglobulin gamma-ChainsMolecular ChaperonesCrystallography, X-RayNeurodegenerative DiseasesSpectrometry, FluorescenceOptical Rotatory DispersionProtein DenaturationMagnetic Resonance SpectroscopyKineticsCarrier ProteinsSolutionsHydrogen BondingNuclear ProteinsSilica GelRecombinant ProteinsProteostasis DeficienciesTemperatureHydrogen-Ion ConcentrationHuntington DiseaseMyoglobinModels, ChemicalMolecular Dynamics SimulationStructure-Activity RelationshipSpinocerebellar AtaxiasCell LineSpectrum Analysis, RamanLigandsTryptophanInclusion BodiesComputer SimulationRepressor ProteinsNuclear Magnetic Resonance, BiomolecularAnilino NaphthalenesulfonatesRecombinant Fusion ProteinsUbiquitinProtein Structure, QuaternarySpectroscopy, Fourier Transform InfraredMutagenesis, Site-DirectedSequence Homology, Amino AcidProtein StabilityTrinucleotide Repeat ExpansionEscherichia coliWaterTRPP Cation ChannelsAmino Acid MotifsAmino Acid SubstitutionMuramidaseApoproteinsMolecular StructureHydrogenPrionsGuanidineSolventsBacteriorhodopsinsModels, BiologicalSpectrophotometry, InfraredStatic Electricityalpha-SynucleinSpectrophotometry, UltravioletSchiff BasesBacterial ProteinsAmyloidSaccharomyces cerevisiaeBiophysicsCOS CellsCatalysisProtein TransportHydrophobic and Hydrophilic InteractionsCloning, MolecularHorsesDeuteriumPeptide FragmentsBase SequenceDimerization