Nose DiseasesDeafnessNoseElectronic NoseNose Deformities, AcquiredHearing Loss, SensorineuralNose NeoplasmsHearing LossCochleaPedigreeGenes, RecessiveEar, InnerSyndromeEvoked Potentials, Auditory, Brain StemConnexinsHearing Loss, UnilateralHair Cells, AuditoryRhinoplastyStria VascularisSpiral GanglionHearingCochlear ImplantsHearing Loss, Bilateral