Huntington DiseaseDuodenoscopyCrohn DiseaseTrinucleotide Repeat ExpansionTrinucleotide RepeatsChromosomes, Human, Pair 4Nerve Tissue ProteinsQuinolinic AcidNuclear ProteinsCorpus StriatumAge of Onset3-Hydroxyanthranilate 3,4-DioxygenaseChoreaProdromal SymptomsRats, TransgenicDisease Models, AnimalWitchcraftNeurodegenerative DiseasesCaudate NucleusGenetic TestingMice, TransgenicAtrophyRotarod Performance TestBrainTetrabenazineNeostriatumMythologyMutationQuinolinic AcidsPeptidesNerve Fibers, UnmyelinatedNeuronsInclusion BodiesPutamenPedigreeChromosome BandingDopamine and cAMP-Regulated Phosphoprotein 32Mutant ProteinsLipoylationGene Knock-In TechniquesPhenotypeGenetic MarkersGenetic CounselingAllelesDisease ProgressionGenetic LinkageNitro CompoundsEarly DiagnosisHeterozygote DetectionMagnetic Resonance ImagingGenotypeNerve DegenerationCognition DisordersChromosome MappingAutophagy