- Perivascular epithelioid cell tumour, also known as PEComa or PEC tumour, is a family of mesenchymal tumours consisting of perivascular epithelioid cells (PECs). (wikipedia.org)
- PECs consist of perivascular epithelioid cells with a clear/granular cytoplasm and central round nucleus without prominent nucleoli. (wikipedia.org)
- A family of mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. (curehunter.com)
- The most common tumours in the PEComa family are renal angiomyolipoma and pulmonary lymphangioleiomyomatosis, both of which are more common in patients with tuberous sclerosis complex. (wikipedia.org)
- Genetically, PECs are linked to the tuberous sclerosis genes TSC1 and TSC2, although this link is stronger for angiomyolipoma and lymphangioleiomyomatosis than for other members of the PEComa family. (wikipedia.org)
- PECs bear significant histologic and immunohistochemical similarity to: angiomyolipoma, clear-cell sugar tumour (CCST), lymphangioleiomyomatosis, and, clear-cell myomelanocytic tumour of ligamentum teres/falciform ligament. (wikipedia.org)
- Launch The perivascular epithelioid cell (PEC) is a cell type that's histologically and immunohistochemically within several tumors, including renal angiomyolipoma (AML), clear-cell glucose tumor (CCST) lymphangioleiomyomatosis (LAM), and rare clear-cell tumors of other anatomical sites. (cell-signaling-pathways.com)
- The World Health Corporation defines PEComa as unusual mesenchymal tumors composed of histologically and immunohistochemically special PECs. (cell-signaling-pathways.com)
- abdominopelvic sarcoma of perivascular epitheloid cells primary extrapulmonary sugar tumour Thus, it has been advocated that the above could be classified PEComas. (wikipedia.org)
- 1] In 1963, Liebow and Castleman[2] initial identified a definite kind of Ruxolitinib distributor benign crystal clear cell tumor known as CCST in the lung. (cell-signaling-pathways.com)
- The same writers coined the word benign apparent cell (glucose) tumor from the lung in 1971. (cell-signaling-pathways.com)
- The cell of origins and various types of obvious cell tumors of the lung (the so-called sugars tumor) have been enigmatic and controversial for the last 3 decades. (cell-signaling-pathways.com)
- The term PEComa was launched by Zamboni et al[4] in 1996 to describe this rare family of morphological, immunohistochemical, and ultrastructural features. (cell-signaling-pathways.com)
- The cell type from which these tumours originate remains unknown. (wikipedia.org)
- Lessons: To the very best of our understanding, this is actually the initial report of the PEComa from the rectum with liver organ metastases treated with just surgical resection. (cell-signaling-pathways.com)
- Many PEComa types shows a female predominance in the sex ratio. (wikipedia.org)
- There have been increasing numbers of reports of different views on and insights into obvious cell tumors in recent years. (cell-signaling-pathways.com)
- Perivascular epithelioid cell tumour, also known as PEComa or PEC tumour, is a family of mesenchymal tumours consisting of perivascular epithelioid cells (PECs). (wikipedia.org)
- PECs bear significant histologic and immunohistochemical similarity to: angiomyolipoma, clear-cell sugar tumour (CCST), lymphangioleiomyomatosis, and, clear-cell myomelanocytic tumour of ligamentum teres/falciform ligament. (wikipedia.org)
- Clear cell "sugar" tumor of the lung: a well-enhanced mass with an early washout pattern on dynamic contrast-enhanced computed tomography. (radiopaedia.org)
- 2. Liebow AA, Castleman B. Benign clear cell ("sugar") tumors of the lung. (radiopaedia.org)
- A rare cause of hemoptysis: benign sugar (clear) cell tumor of the lung. (radiopaedia.org)
- Benign clear (sugar) cell tumor of the lung with CD1a expression. (radiopaedia.org)
- Clear cell tumors of the lung are rare benign pulmonary neoplasms that contain an abundant amount of glycogen. (radiopaedia.org)
- 6. Jordá aragón C, Froufe sánchez A, Padilla alarcón J. [Benign clear cell tumor of the lung]. (radiopaedia.org)